"12" . "Diabetes insipidus n\u00E1sledovan\u00FD po 4 letech dysartri\u00ED a lehkou pravostrannou hemipar\u00E9zou \u2013 prvn\u00ED klinick\u00E9 p\u0159\u00EDznaky Erdheimovy-Chesterovy nemoci. Popis a zobrazen\u00ED p\u0159\u00EDpadu s p\u0159ehledem informac\u00ED o t\u00E9to nemoci"@cs . . "Krej\u010D\u00ED, Marta" . . . . "Pour, L." . "Erdheim-Chester disease"@en . "Diabetes insipidus n\u00E1sledovan\u00FD po 4 letech dysartri\u00ED a lehkou pravostrannou hemipar\u00E9zou \u2013 prvn\u00ED klinick\u00E9 p\u0159\u00EDznaky Erdheimovy-Chesterovy nemoci. Popis a zobrazen\u00ED p\u0159\u00EDpadu s p\u0159ehledem informac\u00ED o t\u00E9to nemoci" . . . "0042-773X" . . . "17"^^ . . "In 2004, diabetes insipidus was the first clinical sign of Erdheim-Chester disease in our patient. The disease is associated with elevated inflammatory parameters: leucocytosis, thrombocytosis, elevated CRP fibrinogen levels. Diagnosis was verified following histological assessment of iliac bone marrow, where focal infiltrations with foamy histiocytes of typicalimmunophenotype (CD68+, CD1a\u2013, S100\u2013) were confirmed. Treatment was initiated with chemotherapy consisting of 2 g/m2 of cyclophosphamide on day 1 and 200 mg/m2 of etoposide IV infusion on days 1\u20133, and followed by administration of 5 \u00B5g/kg of G-CSF and collection of haematopoietic peripheral blood stem cells (PBSC). PBSC collection was followed by 5-day administration of 5 mg/m2/day of 2-chlorodeoxyadenosine (Litac) administered to the patient at monthly intervals."@en . "6"^^ . "CZ - \u010Cesk\u00E1 republika" . . . "Vnit\u0159n\u00ED l\u00E9ka\u0159stsv\u00ED" . . . "Diabetes insipidus n\u00E1sledovan\u00FD po 4 letech dysartri\u00ED a lehkou pravostrannou hemipar\u00E9zou \u2013 prvn\u00ED klinick\u00E9 p\u0159\u00EDznaky Erdheimovy-Chesterovy nemoci. Popis a zobrazen\u00ED p\u0159\u00EDpadu s p\u0159ehledem informac\u00ED o t\u00E9to nemoci"@cs . . "[B8AD5AF3CE52]" . "P(LC06027), V, Z(MSM0021622434)" . "Diabetes insipidus followed, after 4 years, with dysarthria and mild right-sided hemiparesis--the first clinical signs of Erdheim-Chester disease. Description and depiction of a case with a review of information on the disease"@en . "Diabetes insipidus n\u00E1sledovan\u00FD po 4 letech dysartri\u00ED a lehkou pravostrannou hemipar\u00E9zou \u2013 prvn\u00ED klinick\u00E9 p\u0159\u00EDznaky Erdheimovy-Chesterovy nemoci. Popis a zobrazen\u00ED p\u0159\u00EDpadu s p\u0159ehledem informac\u00ED o t\u00E9to nemoci" . "H\u00E1jek, Roman" . "Mayer, Ji\u0159\u00ED" . . . . . "Prvn\u00EDm klinick\u00FDm p\u0159\u00EDznakem Erdheimovy-Chesterovy nemoci u na\u0161eho pacienta byl v roce 2004 diabetes insipidus. Diagn\u00F3za byla stanovena histologick\u00FDm hodnocen\u00EDm kostn\u00ED d\u0159en\u011B z\u00EDskan\u00E9 z lopaty kosti p\u00E1nevn\u00ED, v n\u00ED\u017E byla prok\u00E1z\u00E1na lo\u017Eiskov\u00E1 infiltrace p\u011Bnit\u00FDmi histiocyty s typick\u00FDm imunofenotypem (CD68+, CD1a\u2013, S100\u2013). L\u00E9\u010Dba byla zah\u00E1jena chemoterapi\u00ED cyklofosfamidem 2 g/m2 den 1 a etoposidem 200 mg/m2 i.v. infuze den 1\u20133, s n\u00E1slednou aplikac\u00ED G-CSF v d\u00E1vce 5 \u00B5g/kg a sb\u011Brem kmenov\u00FDch krvetvorn\u00FDch bun\u011Bk z perifern\u00ED krve (PBSC). Po sb\u011Bru PBSC byla zah\u00E1jena aplikace 2-chlordeoxyadenosinu (Litac), v d\u00E1vce 5 mg/m2 s.c., cyklofosfamidu 150 mg/m2 i.v. a dexametazonu 24 mg i.v., v\u0161e 1.\u20135. den. Tyto cykly se opakovaly po 28 dnech, celkem 6kr\u00E1t. \u00DA\u010Dinnost l\u00E9\u010Dby byla hodnocena kontroln\u00EDm celot\u011Blov\u00FDm PET-CT, celot\u011Blov\u00FDm MR zobrazen\u00EDm s difuz\u00ED, scintigrafi\u00ED skeletu a MR zobrazen\u00EDm CNS. Po 6 cyklech chemoterapie z\u016Fst\u00E1v\u00E1 patologick\u00FD n\u00E1lez v dlouh\u00FDch kostech beze zm\u011Bny."@cs . "RIV/65269705:_____/09:#0000732!RIV10-MZ0-65269705" . . "K\u0159en, Leo\u0161" . . "Prvn\u00EDm klinick\u00FDm p\u0159\u00EDznakem Erdheimovy-Chesterovy nemoci u na\u0161eho pacienta byl v roce 2004 diabetes insipidus. Diagn\u00F3za byla stanovena histologick\u00FDm hodnocen\u00EDm kostn\u00ED d\u0159en\u011B z\u00EDskan\u00E9 z lopaty kosti p\u00E1nevn\u00ED, v n\u00ED\u017E byla prok\u00E1z\u00E1na lo\u017Eiskov\u00E1 infiltrace p\u011Bnit\u00FDmi histiocyty s typick\u00FDm imunofenotypem (CD68+, CD1a\u2013, S100\u2013). L\u00E9\u010Dba byla zah\u00E1jena chemoterapi\u00ED cyklofosfamidem 2 g/m2 den 1 a etoposidem 200 mg/m2 i.v. infuze den 1\u20133, s n\u00E1slednou aplikac\u00ED G-CSF v d\u00E1vce 5 \u00B5g/kg a sb\u011Brem kmenov\u00FDch krvetvorn\u00FDch bun\u011Bk z perifern\u00ED krve (PBSC). Po sb\u011Bru PBSC byla zah\u00E1jena aplikace 2-chlordeoxyadenosinu (Litac), v d\u00E1vce 5 mg/m2 s.c., cyklofosfamidu 150 mg/m2 i.v. a dexametazonu 24 mg i.v., v\u0161e 1.\u20135. den. Tyto cykly se opakovaly po 28 dnech, celkem 6kr\u00E1t. \u00DA\u010Dinnost l\u00E9\u010Dby byla hodnocena kontroln\u00EDm celot\u011Blov\u00FDm PET-CT, celot\u011Blov\u00FDm MR zobrazen\u00EDm s difuz\u00ED, scintigrafi\u00ED skeletu a MR zobrazen\u00EDm CNS. Po 6 cyklech chemoterapie z\u016Fst\u00E1v\u00E1 patologick\u00FD n\u00E1lez v dlouh\u00FDch kostech beze zm\u011Bny." . "Adam, Zden\u011Bk" . "310134" . . "RIV/65269705:_____/09:#0000732" . "16"^^ . "Diabetes insipidus followed, after 4 years, with dysarthria and mild right-sided hemiparesis--the first clinical signs of Erdheim-Chester disease. Description and depiction of a case with a review of information on the disease"@en . "55" .