"Adamus, Milan" . "RIV/61989592:15110/14:33151701" . "RIV/61989592:15110/14:33151701!RIV15-MSM-15110___" . "[17240CED4B58]" . "Marfan\u016Fv syndrom je vrozen\u00E1 porucha pojiva postihuj\u00EDc\u00ED p\u0159edev\u0161\u00EDm kardiovaskul\u00E1rn\u00ED, respira\u010Dn\u00ED a pohybov\u00FD syst\u00E9m. Disekce dilatovan\u00E9 proxim\u00E1ln\u00ED aorty je nejz\u00E1va\u017En\u011Bj\u0161\u00ED komplikac\u00ED a je spojena s vysokou mortalitou. T\u011Bhotenstv\u00ED a peripart\u00E1ln\u00ED obdob\u00ED jsou v tomto ohledu zvl\u00E1\u0161\u0165 kritick\u00E9 a p\u0159in\u00E1\u0161ej\u00ED zv\u00FD\u0161en\u00E9 riziko akutn\u00ED aort\u00E1ln\u00ED disekce. Porodnick\u00E1 p\u00E9\u010De o pacientkys Marfanov\u00FDm syndromem p\u0159edstavuje speci\u00E1ln\u00ED a komplexn\u00ED mezioborovou problematiku. Jeliko\u017E je pacientsk\u00E1 populace rodi\u010Dek s Marfanov\u00FDm syndromem \u00FAzk\u00E1 (a\u017E raritn\u00ED), jsou klinick\u00E9 zku\u0161enosti omezen\u00E9, a to i v p\u0159\u00EDpad\u011B specializovan\u00FDch center. Stejn\u00FDm zp\u016Fsobem jsou limitovan\u00E9 i v sou\u010Dasnosti dostupn\u00E9 liter\u00E1rn\u00ED zdroje t\u00FDkaj\u00EDc\u00ED se problematiky peripart\u00E1ln\u00ED p\u00E9\u010De u t\u011Bchto pacientek. V \u010Dl\u00E1nku je prezentov\u00E1na kazuistika 18let\u00E9 t\u011Bhotn\u00E9 pacientky s diagn\u00F3zou Marfanova syndromu, u n\u00ED\u017E byl porod bez komplikac\u00ED veden elektivn\u00EDm c\u00EDsa\u0159sk\u00FDm \u0159ezem v region\u00E1ln\u00ED anestezii v 34. t\u00FDdnu gravidity. V navazuj\u00EDc\u00EDm p\u0159ehledu byly analyzov\u00E1ny dostupn\u00E9 relevantn\u00ED pr\u00E1ce zab\u00FDvaj\u00EDc\u00ED se problematikou anestezie t\u011Bhotn\u00FDch s Marfanov\u00FDm syndromem."@cs . "Axmann, Karel" . . . "15110" . . . "5" . "Marfan\u016Fv syndrom je vrozen\u00E1 porucha pojiva postihuj\u00EDc\u00ED p\u0159edev\u0161\u00EDm kardiovaskul\u00E1rn\u00ED, respira\u010Dn\u00ED a pohybov\u00FD syst\u00E9m. Disekce dilatovan\u00E9 proxim\u00E1ln\u00ED aorty je nejz\u00E1va\u017En\u011Bj\u0161\u00ED komplikac\u00ED a je spojena s vysokou mortalitou. T\u011Bhotenstv\u00ED a peripart\u00E1ln\u00ED obdob\u00ED jsou v tomto ohledu zvl\u00E1\u0161\u0165 kritick\u00E9 a p\u0159in\u00E1\u0161ej\u00ED zv\u00FD\u0161en\u00E9 riziko akutn\u00ED aort\u00E1ln\u00ED disekce. Porodnick\u00E1 p\u00E9\u010De o pacientkys Marfanov\u00FDm syndromem p\u0159edstavuje speci\u00E1ln\u00ED a komplexn\u00ED mezioborovou problematiku. Jeliko\u017E je pacientsk\u00E1 populace rodi\u010Dek s Marfanov\u00FDm syndromem \u00FAzk\u00E1 (a\u017E raritn\u00ED), jsou klinick\u00E9 zku\u0161enosti omezen\u00E9, a to i v p\u0159\u00EDpad\u011B specializovan\u00FDch center. Stejn\u00FDm zp\u016Fsobem jsou limitovan\u00E9 i v sou\u010Dasnosti dostupn\u00E9 liter\u00E1rn\u00ED zdroje t\u00FDkaj\u00EDc\u00ED se problematiky peripart\u00E1ln\u00ED p\u00E9\u010De u t\u011Bchto pacientek. V \u010Dl\u00E1nku je prezentov\u00E1na kazuistika 18let\u00E9 t\u011Bhotn\u00E9 pacientky s diagn\u00F3zou Marfanova syndromu, u n\u00ED\u017E byl porod bez komplikac\u00ED veden elektivn\u00EDm c\u00EDsa\u0159sk\u00FDm \u0159ezem v region\u00E1ln\u00ED anestezii v 34. t\u00FDdnu gravidity. V navazuj\u00EDc\u00EDm p\u0159ehledu byly analyzov\u00E1ny dostupn\u00E9 relevantn\u00ED pr\u00E1ce zab\u00FDvaj\u00EDc\u00ED se problematikou anestezie t\u011Bhotn\u00FDch s Marfanov\u00FDm syndromem." . "1214-2158" . "I" . . "Periopera\u010Dn\u00ED management c\u00EDsa\u0159sk\u00E9ho \u0159ezu u rodi\u010Dky s Marfanov\u00FDm syndromem - kazuistika a systematick\u00FD p\u0159ehled literatury" . "2"^^ . . . . "Periopera\u010Dn\u00ED management c\u00EDsa\u0159sk\u00E9ho \u0159ezu u rodi\u010Dky s Marfanov\u00FDm syndromem - kazuistika a systematick\u00FD p\u0159ehled literatury"@cs . . "Periopera\u010Dn\u00ED management c\u00EDsa\u0159sk\u00E9ho \u0159ezu u rodi\u010Dky s Marfanov\u00FDm syndromem - kazuistika a systematick\u00FD p\u0159ehled literatury" . "1"^^ . . "anaesthesia; Caesarean Section; pregnancy; Marfan syndrome"@en . "25" . "CZ - \u010Cesk\u00E1 republika" . . . "Periopera\u010Dn\u00ED management c\u00EDsa\u0159sk\u00E9ho \u0159ezu u rodi\u010Dky s Marfanov\u00FDm syndromem - kazuistika a systematick\u00FD p\u0159ehled literatury"@cs . "Perioperative management of Caesarean Section in a parturient with Marfan syndrome - case report and systemic review of literature"@en . "Perioperative management of Caesarean Section in a parturient with Marfan syndrome - case report and systemic review of literature"@en . . "Marfan syndrome is an inherited disease affecting mainly the cardiovascular, respiratory and muskuloskeletal systems. Aortic dilatation and dissection is the major cardiovascular complication associated with high mortality. Pregnancy and peripartum are a critical period accelerating the risk of acute aortic dissection. Peripartum management of patients with Marfan syndrome represents a special complex multidisciplinary issue. Due to the rare diagnosis and small patient population, the clinical experience is limited even in specialized centers. Up-to-date literary resources regarding paripartum care of patients with Marfan syndrome are also scarce. We present a case-report of an 18-year old partiturient with the diagnosis of Marfan syndrome who underwent uncomplicated Caesarean Section in regional anaesthesia in the 34th gestational week. Systematic literature review is included, analyzing the recent available papers on anaesthesia for Casarean Section in patients with Marfan syndrome."@en . "36201" . . "5"^^ . "Anesteziologie & intenzivn\u00ED medic\u00EDna" . .