"RIV/61989592:15110/07:00004041!RIV08-MSM-15110___" . . . . . . . . "Budd ? Chiari syndrom ? the patient with polycythemia vera"@en . "\u00DAst\u00ED nad Labem" . . "5"^^ . "BOS. org. s. r. o. , \u00DAst\u00ED nad Labem" . "412336" . "5"^^ . . "Budd-Chiariho syndrom u nemocn\u00E9 s prim\u00E1rn\u00ED polycyt\u00E9mi\u00ED" . "48-49" . "Budd ? Chiari syndrom ? the patient with polycythemia vera"@en . "Vinklerov\u00E1, Ilona" . "S" . . "RIV/61989592:15110/07:00004041" . . "[243BE000FC81]" . "Prim\u00E1rn\u00ED polycytemie je myeloprolifera\u010Dn\u00ED onemocn\u011Bn\u00ED s prevalenc\u00ED kolem 5/1 000 000 obyvatel. Jedn\u00E1 se trombofiln\u00ED stav a tromb\u00F3za je nej\u010Dast\u011Bj\u0161\u00ED p\u0159\u00ED\u010Dinou smrti pacient\u016F s prim\u00E1rn\u00ED polycytemi\u00ED. Jednou z typick\u00FDch komplikac\u00ED je Budd-Chiariho syndrom, kter\u00FD je charakterizov\u00E1n blok\u00E1dou krevn\u00EDho toku jatern\u00EDch \u017Eil, v\u011Bt\u0161inou pr\u00E1v\u011B na podklad\u011B tromb\u00F3zy."@cs . . "Polycythemia vera (PV) is a myeloproliferative disease with a prevalence about 5/1.000.000. There is a high risk of thrombosis in the group of patient with PV and the thrombosis is the most common cause of death. One of the typical complication of PV is Budd ? Chiari syndrom (BCS) , characterized by the hepatic venous outflow occlusion, frequently caused by thrombosis. BCS can be caused by PV in 60%. But the recent studies reported the number 10-40%. The is a lot of other causes of BCS. We report the case of a young woman with personal history of primary polycythemia, which was treated by interferon (INF). We detected Budd ? Chiari syndrom and transjugular intrahepatic portosystemic shunt (TIPS) was used as treatment. In the few years after stenting, even there were no shunt dysfunction, the big oesofageal (more then 5mm) and also fundal varices appear. We found out the liver cirrhosis by histology and the patient is indicated to liver transplantation."@en . "Gregar, Jan" . "Prim\u00E1rn\u00ED polycytemie je myeloprolifera\u010Dn\u00ED onemocn\u011Bn\u00ED s prevalenc\u00ED kolem 5/1 000 000 obyvatel. Jedn\u00E1 se trombofiln\u00ED stav a tromb\u00F3za je nej\u010Dast\u011Bj\u0161\u00ED p\u0159\u00ED\u010Dinou smrti pacient\u016F s prim\u00E1rn\u00ED polycytemi\u00ED. Jednou z typick\u00FDch komplikac\u00ED je Budd-Chiariho syndrom, kter\u00FD je charakterizov\u00E1n blok\u00E1dou krevn\u00EDho toku jatern\u00EDch \u017Eil, v\u011Bt\u0161inou pr\u00E1v\u011B na podklad\u011B tromb\u00F3zy." . . . "XI. Hradeck\u00E9 gastroenterologick\u00E9 dny" . . "978-80-239-8866-6" . . "15110" . . "Budd-Chiariho syndrom u nemocn\u00E9 s prim\u00E1rn\u00ED polycyt\u00E9mi\u00ED"@cs . . "64"^^ . "Budd-Chiariho syndrom u nemocn\u00E9 s prim\u00E1rn\u00ED polycyt\u00E9mi\u00ED" . "Proch\u00E1zka, Vlastimil" . . "Tozzi, Igor" . "Budd-Chiari syndrome (BCS); polycythemia vera (PV); thrombosis; interferon (INF); transjugular intrahepatic portosystemic shunt (TIPS); liver transplantation"@en . . "Hlu\u0161\u00ED, Anton\u00EDn" . . "Budd-Chiariho syndrom u nemocn\u00E9 s prim\u00E1rn\u00ED polycyt\u00E9mi\u00ED"@cs .