"Bortl\u00ED\u010Dek, Zbyn\u011Bk" . "0042-773X" . . . . "RIV/00216224:14110/14:00076122" . "Erdheim-Chester disease is a very rare histiocytic disease. It represents one form of juvenile xanthogranuloma in WHO classification of blood diseases. The disease often causes B symptoms, skeletal pain and also may cause diabetes insipidus and retroperitoneal fibrosis. Selection of therapy depends on published case reports and small clinical trials. There are no recommendations for treatment based on randomized studies. Interferon a is probably the most commonly used drug for this disease. Some remissions have been described after treatment. However,long-term interferon a application is needed which is associated with numerous side effects. There are limited experiences with clabridine in this indication. In Pubmed Medline database, we have found 3 publications dedicated to description of treatment response after cladribine in Erdheim-Chester disease and other 7 papers evaluating effect of cladribine on juvenile xanthogranuloma forms, mostly with positive outcome."@en . . "\u0158eh\u00E1k, Zden\u011Bk" . "anakinra; cladribine; Erdheim-Chester disease; interferon; juvenile xanthogranuloma; PET-CT in diagnosis of fever of unknown origin; vemurafenib; 2-chlorodeoxydenosin"@en . "Vnit\u0159n\u00ED l\u00E9ka\u0159stv\u00ED" . . . . "Nebesk\u00FD, Tom\u00E1\u0161" . . "Krej\u010D\u00ED, Marta" . "[E4A60F424B7D]" . "60" . . "Pr\u00E1\u0161ek, Ji\u0159\u00ED" . . "PET-CT dokumentovan\u00E1 kompletn\u00ED 4let\u00E1 remise Erdheimovy-Chesterovy nemoci po l\u00E9\u010Db\u011B kladribinem" . "Adam, Zden\u011Bk" . "Szturz, Petr" . "36332" . "S" . "Erdheimova-Chesterova nemoc je onemocn\u011Bn\u00ED pat\u0159\u00EDc\u00ED mezi velmi vz\u00E1cn\u00E9 histiocyt\u00E1rn\u00ED choroby. P\u0159edstavuje jednu z forem chorob, \u0159azen\u00FDch posledn\u00ED WHO klasifikac\u00ED krevn\u00EDch chorob do skupiny juveniln\u00EDho xantogranulomu. Nemoc \u010Dasto p\u016Fsob\u00ED B symptomy, d\u00E1le bolesti skeletu a m\u016F\u017Ee zp\u016Fsobit i diabetes insipidus i fibr\u00F3zu retroperitonea. V\u00FDb\u011Br l\u00E9\u010Debn\u00FDch postup\u016F se odv\u00EDj\u00ED od publikovan\u00FDch popis\u016F p\u0159\u00EDpad\u016F \u010Di mal\u00FDch skupin pacient\u016F. Pro tuto nemoc neexistuje l\u00E9\u010Debn\u00E9 doporu\u010Den\u00ED zalo\u017Een\u00E9 na randomizovan\u00FDch studi\u00EDch. Interferon alfa je z\u0159ejm\u011B nej\u010Dast\u011Bji pou\u017E\u00EDvan\u00FD l\u00E9k pro tuto nemoc, byly po n\u011Bm pops\u00E1ny remise. Je v\u0161ak nutn\u00E1 dlouhodob\u00E1 aplikace interferonu alfa a ta je spojena s \u010Detn\u00FDmi ne\u017E\u00E1douc\u00EDmi \u00FA\u010Dinky. Zku\u0161enost\u00ED s kladribinem v t\u00E9to indikaci je o n\u011Bco m\u00E9n\u011B. V datab\u00E1zi Medline Pubmed jsme nalezli 3 publikace popisuj\u00EDc\u00ED l\u00E9\u010Debnou odezvu po kladribinu u Erdheimovy-Chesterovy nemoci a 7 dal\u0161\u00EDch publikac\u00ED, hodnot\u00EDc\u00EDch \u00FA\u010Dinek kladribinu u n\u011Bkter\u00E9 z forem juveniln\u00EDho xantogranulomu, p\u0159ev\u00E1\u017En\u011B s pozitivn\u00EDm v\u00FDsledkem."@cs . "Pour, Lud\u011Bk" . "Mayer, Ji\u0159\u00ED" . . "12"^^ . "PET-CT dokumentovan\u00E1 kompletn\u00ED 4let\u00E1 remise Erdheimovy-Chesterovy nemoci po l\u00E9\u010Db\u011B kladribinem" . "13"^^ . "PET-CT dokumentovan\u00E1 kompletn\u00ED 4let\u00E1 remise Erdheimovy-Chesterovy nemoci po l\u00E9\u010Db\u011B kladribinem"@cs . . "RIV/00216224:14110/14:00076122!RIV15-MSM-14110___" . . . "8"^^ . "Erdheimova-Chesterova nemoc je onemocn\u011Bn\u00ED pat\u0159\u00EDc\u00ED mezi velmi vz\u00E1cn\u00E9 histiocyt\u00E1rn\u00ED choroby. P\u0159edstavuje jednu z forem chorob, \u0159azen\u00FDch posledn\u00ED WHO klasifikac\u00ED krevn\u00EDch chorob do skupiny juveniln\u00EDho xantogranulomu. Nemoc \u010Dasto p\u016Fsob\u00ED B symptomy, d\u00E1le bolesti skeletu a m\u016F\u017Ee zp\u016Fsobit i diabetes insipidus i fibr\u00F3zu retroperitonea. V\u00FDb\u011Br l\u00E9\u010Debn\u00FDch postup\u016F se odv\u00EDj\u00ED od publikovan\u00FDch popis\u016F p\u0159\u00EDpad\u016F \u010Di mal\u00FDch skupin pacient\u016F. Pro tuto nemoc neexistuje l\u00E9\u010Debn\u00E9 doporu\u010Den\u00ED zalo\u017Een\u00E9 na randomizovan\u00FDch studi\u00EDch. Interferon alfa je z\u0159ejm\u011B nej\u010Dast\u011Bji pou\u017E\u00EDvan\u00FD l\u00E9k pro tuto nemoc, byly po n\u011Bm pops\u00E1ny remise. Je v\u0161ak nutn\u00E1 dlouhodob\u00E1 aplikace interferonu alfa a ta je spojena s \u010Detn\u00FDmi ne\u017E\u00E1douc\u00EDmi \u00FA\u010Dinky. Zku\u0161enost\u00ED s kladribinem v t\u00E9to indikaci je o n\u011Bco m\u00E9n\u011B. V datab\u00E1zi Medline Pubmed jsme nalezli 3 publikace popisuj\u00EDc\u00ED l\u00E9\u010Debnou odezvu po kladribinu u Erdheimovy-Chesterovy nemoci a 7 dal\u0161\u00EDch publikac\u00ED, hodnot\u00EDc\u00EDch \u00FA\u010Dinek kladribinu u n\u011Bkter\u00E9 z forem juveniln\u00EDho xantogranulomu, p\u0159ev\u00E1\u017En\u011B s pozitivn\u00EDm v\u00FDsledkem." . . "5-6" . . "PET-CT dokumentovan\u00E1 kompletn\u00ED 4let\u00E1 remise Erdheimovy-Chesterovy nemoci po l\u00E9\u010Db\u011B kladribinem"@cs . . . . . . "Kr\u00E1l, Zden\u011Bk" . . "CZ - \u010Cesk\u00E1 republika" . . "Koukalov\u00E1, Renata" . "PET-CT documented complete remission of Erdheim-Chester disease, lasting more than 4 years from treatment initiation with cladribine"@en . . . "PET-CT documented complete remission of Erdheim-Chester disease, lasting more than 4 years from treatment initiation with cladribine"@en . . "Adamov\u00E1, Zdenka" . "14110" .