"Tranzitorn\u00ED pseudohypoaldosteronismus - nefro-urologick\u00E9 %22puzzle%22" . "6"^^ . "Zerhau, Pavel" . . . . "RIV/00216224:14110/14:00075231" . "Transient pseudohypoaldosteronism - %22puzzle%22 of pediatric nephrology and urology"@en . "Transient pseudohypoaldosteronism \u2013 \u201Epuzzle\u201C of pediatric nephrology and urology In childhood the majority of changes in serum electrolytes concerns dysbalance of sodium and potassium. Hyponatremia accompanied by hyperkalemia is usually associated with disorders of the adrenal glands, but may also occur in the course of kidney diseases or disorders of gastrointestinal tract. Pseudohypoaldosteronism is an example of salt-losing syndrome and is characterized by hyponatremia, hyperkalemia, metabolic acidosis, high serum aldosterone and high plasma renin. One type of this condition is transient pseudohypoaldosteronism type I. Its development occurs most frequently in neonates or infants in association with urinary tract infections and/or urinary tract anomalies. We present a group of 14 children (6 girls, 8 boys, mean age 5."@en . "9"^^ . "69" . "Tranzitorn\u00ED pseudohypoaldosteronismus - nefro-urologick\u00E9 %22puzzle%22"@cs . "0069-2328" . "6"^^ . . "Jaband\u017Eiev, Petr" . "Transient pseudohypoaldosteronism - %22puzzle%22 of pediatric nephrology and urology"@en . "V d\u011Btsk\u00E9m v\u011Bku se v\u011Bt\u0161ina zm\u011Bn s\u00E9rov\u00E9 koncentrace elektrolyt\u016F t\u00FDk\u00E1 dysbalance sod\u00EDku a drasl\u00EDku. Hyponatr\u00E9mie prov\u00E1zen\u00E1 hyperkal\u00E9mi\u00ED je nej\u010Dast\u011Bji asociov\u00E1na s chorobami nadledvin, m\u016F\u017Ee v\u0161ak vzniknout tak\u00E9 p\u0159i poruch\u00E1ch homeost\u00E1zy t\u011Blesn\u00E9 vody a miner\u00E1l\u016F v pr\u016Fb\u011Bhu onemocn\u011Bn\u00ED ledvin nebo za\u017E\u00EDvac\u00EDho \u00FAstroj\u00ED. Pseudohypoaldosteronismus je syndromem ren\u00E1ln\u00EDch soln\u00FDch ztr\u00E1t, kter\u00E9 jsou sou\u010Dasn\u011B prov\u00E1zeny hyponatr\u00E9mi\u00ED, hyperkal\u00E9mi\u00ED, metabolickou acid\u00F3zou a zv\u00FD\u0161enou s\u00E9rovou koncentrac\u00ED aldosteronu a reninu. Jednou z variant tohoto stavu je tranzitorn\u00ED pseudohypoaldosteronismus typ I. K jeho rozvoji doch\u00E1z\u00ED nej\u010Dast\u011Bji u novorozenc\u016F nebo kojenc\u016F a to v souvislosti s infekc\u00ED mo\u010Dov\u00FDch cest a/nebo obstruk\u010Dn\u00EDmi uropatiemi. Uveden je soubor 14 d\u011Bt\u00ED (6 d\u00EDvek, 8 chlapc\u016F, pr\u016Fm\u011Brn\u00FD v\u011Bk 5,6 m\u011Bs\u00EDc\u016F) s tranzitorn\u00EDm pseudohypoaldosteronismem typ I, kde u 12 z nich byla vyvol\u00E1vaj\u00EDc\u00ED p\u0159\u00ED\u010Dinou anom\u00E1lie mo\u010Dov\u00FDch cest prov\u00E1zen\u00E1 infekc\u00ED, u 2 d\u011Bt\u00ED akutn\u00ED pyelonefritida bez abnormit dut\u00E9ho syst\u00E9mu ledvin." . . "51123" . "Dole\u017Eel, Zden\u011Bk" . . . . "R\u00E1\u010Dilov\u00E1, Zde\u0148ka" . . "Dost\u00E1lkov\u00E1, Dana" . . "transient pseudohypoaldosteronism; urinary tract infection; obstructive uropathy"@en . "1" . . . . "V d\u011Btsk\u00E9m v\u011Bku se v\u011Bt\u0161ina zm\u011Bn s\u00E9rov\u00E9 koncentrace elektrolyt\u016F t\u00FDk\u00E1 dysbalance sod\u00EDku a drasl\u00EDku. Hyponatr\u00E9mie prov\u00E1zen\u00E1 hyperkal\u00E9mi\u00ED je nej\u010Dast\u011Bji asociov\u00E1na s chorobami nadledvin, m\u016F\u017Ee v\u0161ak vzniknout tak\u00E9 p\u0159i poruch\u00E1ch homeost\u00E1zy t\u011Blesn\u00E9 vody a miner\u00E1l\u016F v pr\u016Fb\u011Bhu onemocn\u011Bn\u00ED ledvin nebo za\u017E\u00EDvac\u00EDho \u00FAstroj\u00ED. Pseudohypoaldosteronismus je syndromem ren\u00E1ln\u00EDch soln\u00FDch ztr\u00E1t, kter\u00E9 jsou sou\u010Dasn\u011B prov\u00E1zeny hyponatr\u00E9mi\u00ED, hyperkal\u00E9mi\u00ED, metabolickou acid\u00F3zou a zv\u00FD\u0161enou s\u00E9rovou koncentrac\u00ED aldosteronu a reninu. Jednou z variant tohoto stavu je tranzitorn\u00ED pseudohypoaldosteronismus typ I. K jeho rozvoji doch\u00E1z\u00ED nej\u010Dast\u011Bji u novorozenc\u016F nebo kojenc\u016F a to v souvislosti s infekc\u00ED mo\u010Dov\u00FDch cest a/nebo obstruk\u010Dn\u00EDmi uropatiemi. Uveden je soubor 14 d\u011Bt\u00ED (6 d\u00EDvek, 8 chlapc\u016F, pr\u016Fm\u011Brn\u00FD v\u011Bk 5,6 m\u011Bs\u00EDc\u016F) s tranzitorn\u00EDm pseudohypoaldosteronismem typ I, kde u 12 z nich byla vyvol\u00E1vaj\u00EDc\u00ED p\u0159\u00ED\u010Dinou anom\u00E1lie mo\u010Dov\u00FDch cest prov\u00E1zen\u00E1 infekc\u00ED, u 2 d\u011Bt\u00ED akutn\u00ED pyelonefritida bez abnormit dut\u00E9ho syst\u00E9mu ledvin."@cs . "CZ - \u010Cesk\u00E1 republika" . . "\u0160tarha, Ji\u0159\u00ED" . "Tranzitorn\u00ED pseudohypoaldosteronismus - nefro-urologick\u00E9 %22puzzle%22" . "14110" . "\u010Cesko-slovensk\u00E1 pediatrie" . "I" . . . "[55FE098CB781]" . "RIV/00216224:14110/14:00075231!RIV15-MSM-14110___" . "Tranzitorn\u00ED pseudohypoaldosteronismus - nefro-urologick\u00E9 %22puzzle%22"@cs . . . .