. "Perioral myoclonia with absences (PMA) is a syndrome that belongs to the group of idiopathic generalized epilepsies; however, it is not recognized as a separate entity by the current classification. PMA is marked by typical absences and perioral myoclonias characterized by pouting of the lips or twitching of the corners of the mouth, less frequently by rhythmic movements of the lower jaw. PMA is often confused with focal epilepsy, which may have adverse therapeutic consequences. Two case reports of patients with PMA are presented, accompanied by a video recording. The article also deals with the differential diagnosis and treatment of this syndrome."@en . . "RIV/00216224:14110/13:00071957!RIV14-MSM-14110___" . "Perioral myoclonia with absences: video case reports"@en . . "Neurologie pro praxi" . . "14110" . "1" . "2"^^ . "Perior\u00E1ln\u00ED myoklonie s absencemi \u2013 videokazuistiky"@cs . "Perior\u00E1ln\u00ED myoklonie s absencemi (PMA) je syndrom, kter\u00FD se \u0159ad\u00ED do skupiny idiopatick\u00FDch generalizovan\u00FDch epilepsi\u00ED, av\u0161ak nen\u00ED v sou\u010Dasnosti platnou klasifikac\u00ED uzn\u00E1v\u00E1n jako samostatn\u00E1 jednotka. PMA je charakterizov\u00E1n typick\u00FDmi absencemi a perior\u00E1ln\u00EDmi myokloniemi, je\u017E maj\u00ED charakter \u201E\u0161pulen\u00ED\u201D rt\u016F \u010Di z\u00E1\u0161kub\u016F \u00FAstn\u00EDch koutk\u016F, m\u00E9n\u011B \u010Dasto rytmick\u00FDch pohyb\u016F doln\u00ED \u010Delist\u00ED. PMA je \u010Dasto zam\u011B\u0148ov\u00E1n za fok\u00E1ln\u00ED epilepsii, co\u017E m\u016F\u017Ee m\u00EDt nep\u0159\u00EDzniv\u00E9 terapeutick\u00E9 konsekvence. Uv\u00E1d\u00EDme dv\u011B kazuistiky pacient\u016F s PMA, dopln\u011Bn\u00E9 videoz\u00E1znamem. V \u010Dl\u00E1nku se d\u00E1le v\u011Bnujeme diferenci\u00E1ln\u00ED diagnostice a l\u00E9\u010Db\u011B tohoto syndromu."@cs . "4"^^ . "1"^^ . . "Perior\u00E1ln\u00ED myoklonie s absencemi (PMA) je syndrom, kter\u00FD se \u0159ad\u00ED do skupiny idiopatick\u00FDch generalizovan\u00FDch epilepsi\u00ED, av\u0161ak nen\u00ED v sou\u010Dasnosti platnou klasifikac\u00ED uzn\u00E1v\u00E1n jako samostatn\u00E1 jednotka. PMA je charakterizov\u00E1n typick\u00FDmi absencemi a perior\u00E1ln\u00EDmi myokloniemi, je\u017E maj\u00ED charakter \u201E\u0161pulen\u00ED\u201D rt\u016F \u010Di z\u00E1\u0161kub\u016F \u00FAstn\u00EDch koutk\u016F, m\u00E9n\u011B \u010Dasto rytmick\u00FDch pohyb\u016F doln\u00ED \u010Delist\u00ED. PMA je \u010Dasto zam\u011B\u0148ov\u00E1n za fok\u00E1ln\u00ED epilepsii, co\u017E m\u016F\u017Ee m\u00EDt nep\u0159\u00EDzniv\u00E9 terapeutick\u00E9 konsekvence. Uv\u00E1d\u00EDme dv\u011B kazuistiky pacient\u016F s PMA, dopln\u011Bn\u00E9 videoz\u00E1znamem. V \u010Dl\u00E1nku se d\u00E1le v\u011Bnujeme diferenci\u00E1ln\u00ED diagnostice a l\u00E9\u010Db\u011B tohoto syndromu." . "Perior\u00E1ln\u00ED myoklonie s absencemi \u2013 videokazuistiky" . . . "1335-9592" . . "14" . . "RIV/00216224:14110/13:00071957" . "Kuba, Robert" . "CZ - \u010Cesk\u00E1 republika" . . . "[DDFA1095AE2A]" . "Perior\u00E1ln\u00ED myoklonie s absencemi \u2013 videokazuistiky"@cs . "Perioral myoclonia with absences: video case reports"@en . . "Perior\u00E1ln\u00ED myoklonie s absencemi \u2013 videokazuistiky" . "95811" . . . "P(ED1.1.00/02.0068)" . . . "Dole\u017Ealov\u00E1, Irena" . . "perioral myoclonia with absences; idiopathic generalized epilepsy; typical absences; myoclonia"@en .