"CZ - \u010Cesk\u00E1 republika" . "RIV/00216224:14110/13:00065645!RIV14-MZ0-14110___" . . . "Pour, Lud\u011Bk" . . "PET-CT dokumentovan\u00FD rychl\u00FD n\u00E1stup l\u00E9\u010Debn\u00E9 odpov\u011Bdi cyklofosfamidu, thalidomidu a dexametazonu u multicentrick\u00E9 formy Castlemanovy nemoci. Popis p\u0159\u00EDpadu a p\u0159ehled informac\u00ED o l\u00E9\u010Db\u011B" . . . "Kr\u00E1l, Zden\u011Bk" . . "14110" . . "Hanke, Ivo" . "Castlemanova choroba (zvan\u00E1 t\u00E9\u017E angiofolikul\u00E1rn\u00ED hyperplazie lymfatick\u00FDch uzlin) se d\u011Bl\u00ED na 2 prognosticky odli\u0161n\u00E9 skupiny. Lokalizovan\u00E1 forma je obvykle vyl\u00E9\u010Diteln\u00E1 chirurgick\u00FDm z\u00E1krokem a tedy prognosticky p\u0159\u00EDzniv\u00E1. Multicentrick\u00E1 forma je prognosticky nep\u0159\u00EDzniv\u00E1 a vy\u017Eaduje syst\u00E9movou l\u00E9\u010Dbu. Klasick\u00FDmi projevy multicentrick\u00E9 formy Castlemanovy nemoci je mnoho\u010Detn\u00E9 posti\u017Een\u00ED lymfatick\u00FDch uzlin (lymfadenopatie), n\u011Bkdy b\u00FDv\u00E1 hepatomegalie i splenomegalie a p\u0159\u00EDpadn\u011B v\u00FDpotky v ser\u00F3zn\u00EDch dutin\u00E1ch. K typick\u00FDm patologick\u00FDm laboratorn\u00EDm hodnot\u00E1m u t\u011Bchto pacient\u016F pat\u0159\u00ED zv\u00FD\u0161en\u00E1 hodnota CRP, an\u00E9mie chronick\u00FDch chorob a mnoz\u00ED z nich maj\u00ED zv\u00FD\u0161enou koncentraci celkov\u00E9 b\u00EDlkoviny, p\u0159esahuj\u00EDc\u00ED i 100 g/ l. Je to zp\u016Fsoben\u00E9 vysokou koncentrac\u00ED polyklon\u00E1ln\u00EDch imunoglobulin\u016F. K typick\u00FDm klinick\u00FDm p\u0159\u00EDznak\u016Fm pat\u0159\u00ED kol\u00EDsav\u00E9 subfebrilie \u010Di febrilie, zv\u00FD\u0161en\u00E9 no\u010Dn\u00ED pocen\u00ED, \u00FAnava obvykle souvisej\u00EDc\u00ED s an\u00E9mi\u00ED. U n\u011Bkter\u00FDch pacient\u016F se nemoc projev\u00ED vaskulitidou, \u010Dasto i s posti\u017Een\u00EDm mozkov\u00FDch tepen, tedy c\u00E9vn\u00ED mozkovou p\u0159\u00EDhodou."@cs . . . "PET-CT documented fast onset of treatment response to cyclophosphamide, thalidomide and dexamethasone in patients with multicentric Castleman's disease. Case description and treatment information overview"@en . "0042-773X" . "I, P(NT12130), P(NT12215), P(NT13190)" . "Anaemia of chronic disease; Bortezomib; Castleman's disease; Fever of unknown origin; Multicentric form; Poems syndrome; Polyclonal hypergammaglobulinemia; Rituximab; Thalidomide; Tocilizumab; Vasculitis"@en . . "95960" . . . "\u0158eh\u00E1k, Z." . "Castlemanova choroba (zvan\u00E1 t\u00E9\u017E angiofolikul\u00E1rn\u00ED hyperplazie lymfatick\u00FDch uzlin) se d\u011Bl\u00ED na 2 prognosticky odli\u0161n\u00E9 skupiny. Lokalizovan\u00E1 forma je obvykle vyl\u00E9\u010Diteln\u00E1 chirurgick\u00FDm z\u00E1krokem a tedy prognosticky p\u0159\u00EDzniv\u00E1. Multicentrick\u00E1 forma je prognosticky nep\u0159\u00EDzniv\u00E1 a vy\u017Eaduje syst\u00E9movou l\u00E9\u010Dbu. Klasick\u00FDmi projevy multicentrick\u00E9 formy Castlemanovy nemoci je mnoho\u010Detn\u00E9 posti\u017Een\u00ED lymfatick\u00FDch uzlin (lymfadenopatie), n\u011Bkdy b\u00FDv\u00E1 hepatomegalie i splenomegalie a p\u0159\u00EDpadn\u011B v\u00FDpotky v ser\u00F3zn\u00EDch dutin\u00E1ch. K typick\u00FDm patologick\u00FDm laboratorn\u00EDm hodnot\u00E1m u t\u011Bchto pacient\u016F pat\u0159\u00ED zv\u00FD\u0161en\u00E1 hodnota CRP, an\u00E9mie chronick\u00FDch chorob a mnoz\u00ED z nich maj\u00ED zv\u00FD\u0161enou koncentraci celkov\u00E9 b\u00EDlkoviny, p\u0159esahuj\u00EDc\u00ED i 100 g/ l. Je to zp\u016Fsoben\u00E9 vysokou koncentrac\u00ED polyklon\u00E1ln\u00EDch imunoglobulin\u016F. K typick\u00FDm klinick\u00FDm p\u0159\u00EDznak\u016Fm pat\u0159\u00ED kol\u00EDsav\u00E9 subfebrilie \u010Di febrilie, zv\u00FD\u0161en\u00E9 no\u010Dn\u00ED pocen\u00ED, \u00FAnava obvykle souvisej\u00EDc\u00ED s an\u00E9mi\u00ED. U n\u011Bkter\u00FDch pacient\u016F se nemoc projev\u00ED vaskulitidou, \u010Dasto i s posti\u017Een\u00EDm mozkov\u00FDch tepen, tedy c\u00E9vn\u00ED mozkovou p\u0159\u00EDhodou." . "\u010Cervinkov\u00E1, Ivana" . . "12"^^ . . . . "59" . "Svoboda, Tom\u00E1\u0161" . . "Mayer, Ji\u0159\u00ED" . . "Castleman's disease (also called angiofollicular lymph node hyperplasia) can take two forms with different prognosis: the localized form can usually be treated by a surgical intervention and has therefore a favourable prognosis. On the other hand, the multicentric form has an unfavourable prognosis and requires systemic treatment. Classic manifestations of multicentric Castleman's disease are multiple sites of lymphadenopathy, sometimes hepatomegaly and also splenomegaly or serous cavity effusions. Typical pathological laboratory levels measured in patients with this disease include an increased CRP level, anaemia of chronic diseases, and many patients have an increased total protein concentration, in some cases exceeding even 100g/l. It is caused by a high concentration of polyclonal immunoglobulins. Typical clinical symptoms include fluctuating subfebrile or febrile temperatures, increased night sweats and fatigue usually related to anaemia."@en . "\u0160torkov\u00E1, Tereza" . "PET-CT dokumentovan\u00FD rychl\u00FD n\u00E1stup l\u00E9\u010Debn\u00E9 odpov\u011Bdi cyklofosfamidu, thalidomidu a dexametazonu u multicentrick\u00E9 formy Castlemanovy nemoci. Popis p\u0159\u00EDpadu a p\u0159ehled informac\u00ED o l\u00E9\u010Db\u011B" . "[46D5E76D1E96]" . "Vnit\u0159n\u00ED l\u00E9ka\u0159stv\u00ED" . . "11"^^ . . . . "14"^^ . "PET-CT documented fast onset of treatment response to cyclophosphamide, thalidomide and dexamethasone in patients with multicentric Castleman's disease. Case description and treatment information overview"@en . . . "Penka, Igor" . . . . "Koukalov\u00E1, R." . . "Krej\u010D\u00ED, Marta" . "PET-CT dokumentovan\u00FD rychl\u00FD n\u00E1stup l\u00E9\u010Debn\u00E9 odpov\u011Bdi cyklofosfamidu, thalidomidu a dexametazonu u multicentrick\u00E9 formy Castlemanovy nemoci. Popis p\u0159\u00EDpadu a p\u0159ehled informac\u00ED o l\u00E9\u010Db\u011B"@cs . "RIV/00216224:14110/13:00065645" . . . . . "Szturz, Petr" . . "Adam, Zden\u011Bk" . . . "K\u0159en, Leo\u0161" . "4" . . "PET-CT dokumentovan\u00FD rychl\u00FD n\u00E1stup l\u00E9\u010Debn\u00E9 odpov\u011Bdi cyklofosfamidu, thalidomidu a dexametazonu u multicentrick\u00E9 formy Castlemanovy nemoci. Popis p\u0159\u00EDpadu a p\u0159ehled informac\u00ED o l\u00E9\u010Db\u011B"@cs . .