"600571" . "2"^^ . "cerebellar-olivar; atrophy; dementia"@en . . "Hos\u00E1k, Ladislav" . . "Studie popisuje p\u0159\u00EDpad sedmat\u0159icetilet\u00E9 pacientky s progresivn\u00ED ataxi\u00ED a demenc\u00ED. Pacientka byla hospitalizov\u00E1na na Psychiatrick\u00E9m odd. Fakultn\u00ED nemocnice v Hradci Kr\u00E1lov\u00E9 od b\u0159ezna do dubna 2000. Neurologick\u00E9 symptomy jako porucha ch\u016Fze a \u0159e\u010Di se poprv\u00E9 objevily v roce 1994. Po \u0161esti letech se za\u010Daly objevovat poruchy chov\u00E1n\u00ED spojovan\u00E9 s demenc\u00ED. SPECT sn\u00EDm\u00E1n\u00ED mozku odhalilo cerebel\u00E1rn\u00ED atrofii s hypoperf\u00FAzi a t\u00E9\u017E poruchu perf\u00FAze v pariet\u00E1ln\u00ED k\u016F\u0159e V\u00FDsledky dal\u0161\u00EDch mozkov\u00FDch testov\u00E1n\u00ED (CT, MRI, EEG, neuropsychologie) byly v souladu se SPECT. Pacientka byla l\u00E9\u010Dena kombinac\u00ED psychotropik (piracetam, tiapride, alpha-kotopherol), rehabilitace a podp\u016Frn\u00E9 psychoterapie a mohla b\u00FDt tud\u00ED\u017E z nemocnice propu\u0161t\u011Bna. Po p\u016Fl roce se klinick\u00FD stav v\u00FDrazn\u011B zhor\u0161il. Doposud nebyl \u017E\u00E1dn\u00FD dlouhodob\u00FD l\u00E9k pro SCA vyvinut. Z d\u016Fvodu genetick\u00E9ho charakteru SCA by mohla b\u00FDt v budoucnu genov\u00E1 terapie jednou z mo\u017Enost\u00ED l\u00E9\u010Dby t\u00E9to z\u00E1va\u017En\u00E9 neuropsychiatrick\u00E9 choroby." . . . . "3"^^ . . "S" . "Suppl. 2" . "Cerebelo-oliv\u00E1rn\u00ED atrofie s demenc\u00ED" . . "11150" . "A cerebellar-olivar atrophy with dementia"@en . "Studie popisuje p\u0159\u00EDpad sedmat\u0159icetilet\u00E9 pacientky s progresivn\u00ED ataxi\u00ED a demenc\u00ED. Pacientka byla hospitalizov\u00E1na na Psychiatrick\u00E9m odd. Fakultn\u00ED nemocnice v Hradci Kr\u00E1lov\u00E9 od b\u0159ezna do dubna 2000. Neurologick\u00E9 symptomy jako porucha ch\u016Fze a \u0159e\u010Di se poprv\u00E9 objevily v roce 1994. Po \u0161esti letech se za\u010Daly objevovat poruchy chov\u00E1n\u00ED spojovan\u00E9 s demenc\u00ED. SPECT sn\u00EDm\u00E1n\u00ED mozku odhalilo cerebel\u00E1rn\u00ED atrofii s hypoperf\u00FAzi a t\u00E9\u017E poruchu perf\u00FAze v pariet\u00E1ln\u00ED k\u016F\u0159e V\u00FDsledky dal\u0161\u00EDch mozkov\u00FDch testov\u00E1n\u00ED (CT, MRI, EEG, neuropsychologie) byly v souladu se SPECT. Pacientka byla l\u00E9\u010Dena kombinac\u00ED psychotropik (piracetam, tiapride, alpha-kotopherol), rehabilitace a podp\u016Frn\u00E9 psychoterapie a mohla b\u00FDt tud\u00ED\u017E z nemocnice propu\u0161t\u011Bna. Po p\u016Fl roce se klinick\u00FD stav v\u00FDrazn\u011B zhor\u0161il. Doposud nebyl \u017E\u00E1dn\u00FD dlouhodob\u00FD l\u00E9k pro SCA vyvinut. Z d\u016Fvodu genetick\u00E9ho charakteru SCA by mohla b\u00FDt v budoucnu genov\u00E1 terapie jednou z mo\u017Enost\u00ED l\u00E9\u010Dby t\u00E9to z\u00E1va\u017En\u00E9 neuropsychiatrick\u00E9 choroby."@cs . "73;74" . . "A cerebellar-olivar atrophy with dementia"@en . "Cerebelo-oliv\u00E1rn\u00ED atrofie s demenc\u00ED"@cs . "Urbanov\u00E1, Elen" . "7" . "[3AC4C9B0C88F]" . . . . . . "We describe a case of a thirty-seven-year-old woman patient with a progressive ataxia and dementia. She has been hospitalized at the Dpt. of Psychiatry, University Hospital in Hradec Kr\u00E1lov\u00E9 from March to April 2000. Neurological symptoms as gait and speech impairment appeared in 1994 for the first time. After six years, behavioral disturbances related to dementia also became evident. The results of other brain examinations (CT, MRI, EEG, neuropsychology) were concordant with the SPECT. We successfully treated the patient with a combination of psychotropics (piracetam, tiapride, alpha-tokoferol), rehabilitation, and supportive psychotherapy so that she could have been discharged from the hospital. After half a year, the clinical state significantly worsened. No effective long-term treatment for the SCA patients has been developed as yet. Because of a genetic background of SCA, a gene therapy of this serious neuropsychiatric disease could be considered in the future."@en . . "Psychiatrie" . "Cerebelo-oliv\u00E1rn\u00ED atrofie s demenc\u00ED" . "CZ - \u010Cesk\u00E1 republika" . . "RIV/00216208:11150/03:00004352" . "1211-7579" . "Masopust, Ji\u0159\u00ED" . "Cerebelo-oliv\u00E1rn\u00ED atrofie s demenc\u00ED"@cs . "5"^^ . "RIV/00216208:11150/03:00004352!RIV08-MSM-11150___" . .