. "RIV/00216208:11120/05:00001453!RIV09-MSM-11120___" . . "516207" . "Conjunctivitis lignea: komplikace vrozen\u00E9ho deficitu plazminogenu (kazuistika)"@cs . "Ligneous conjunctivitis: complication of inborn plasminogen deficiency"@en . . "\u0160ach, Josef" . "Ligneous conjunctivitis: complication of inborn plasminogen deficiency"@en . . "Spieka, I." . "1" . . "12"^^ . "Auto\u0159i pod\u00E1vaj\u00ED podrobn\u00FD rozbor desetilet\u00E9ho sledov\u00E1n\u00ED d\u011Btsk\u00E9ho pacienta s conjunctivitis lignea. Dokl\u00E1daj\u00ED p\u0159\u00EDtomnost v\u0161ech, typick\u00FDch o\u010Dn\u00EDch n\u00E1lez\u016F (zejm\u00E9na rekurentn\u00ED tvorbu granulomat\u00F3zn\u00EDch pseudotumor\u016F posti\u017Een\u00E9 sliznice) souvisej\u00EDc\u00EDch s touto vz\u00E1cnou chronickou pseudomembran\u00F3zn\u00ED konjunktivitidou. Klinick\u00FD obraz zahrnuje i deficit plazminogenu, kter\u00FD je nov\u011B pokl\u00E1d\u00E1n za prim\u00E1rn\u00ED p\u0159\u00ED\u010Dinu onemocn\u011Bn\u00ED. Diagn\u00F3za byla potvrzena p\u0159i opakovan\u00FDch exciz\u00EDch histologicky. Typick\u00FD je pseudomembran\u00F3zn\u00ED z\u00E1n\u011Bt se sm\u00ED\u0161en\u00FDm z\u00E1n\u011Btliv\u00FDm infHtr\u00E1tem, kter\u00FD obsahuje velk\u00E9 mno\u017Estv\u00ED element\u016F chronick\u00E9 i akutn\u00ED z\u00E1n\u011Btliv\u00E9 reakce. Sou\u010D\u00E1st\u00ED z\u00E1n\u011Btliv\u00E9ho obrazuje granulom s akumulac\u00ED PAS-pozitivn\u00ED amorfn\u00ED hmoty s vysok\u00FDm obsahem fibrinu a bohatou novotvo\u0159enou c\u00E9vn\u00ED s\u00EDt\u00ED. Na z\u00E1klad\u011B postupn\u011B odhalovan\u00FDch poznatk\u016F o mo\u017En\u00E9 etiopatogenezi onemocn\u011Bn\u00ED se odv\u00EDjel i l\u00E9\u010Debn\u00FD postup v dan\u00E9m obdob\u00ED. Celkov\u011B a\u017E dev\u00E1t\u00FD, posledn\u00ED, chirurgick\u00FD v\u00FDkon p\u0159inesl dlouhodobou remisi trvaj\u00EDc\u00ED ji\u017E t\u0159icet m\u011Bs\u00EDc\u016F. Auto\u0159i kombinovali snesen\u00ED granulomu s"@cs . . . . "CZ - \u010Cesk\u00E1 republika" . "Auto\u0159i pod\u00E1vaj\u00ED podrobn\u00FD rozbor desetilet\u00E9ho sledov\u00E1n\u00ED d\u011Btsk\u00E9ho pacienta s conjunctivitis lignea. Dokl\u00E1daj\u00ED p\u0159\u00EDtomnost v\u0161ech, typick\u00FDch o\u010Dn\u00EDch n\u00E1lez\u016F (zejm\u00E9na rekurentn\u00ED tvorbu granulomat\u00F3zn\u00EDch pseudotumor\u016F posti\u017Een\u00E9 sliznice) souvisej\u00EDc\u00EDch s touto vz\u00E1cnou chronickou pseudomembran\u00F3zn\u00ED konjunktivitidou. Klinick\u00FD obraz zahrnuje i deficit plazminogenu, kter\u00FD je nov\u011B pokl\u00E1d\u00E1n za prim\u00E1rn\u00ED p\u0159\u00ED\u010Dinu onemocn\u011Bn\u00ED. Diagn\u00F3za byla potvrzena p\u0159i opakovan\u00FDch exciz\u00EDch histologicky. Typick\u00FD je pseudomembran\u00F3zn\u00ED z\u00E1n\u011Bt se sm\u00ED\u0161en\u00FDm z\u00E1n\u011Btliv\u00FDm infHtr\u00E1tem, kter\u00FD obsahuje velk\u00E9 mno\u017Estv\u00ED element\u016F chronick\u00E9 i akutn\u00ED z\u00E1n\u011Btliv\u00E9 reakce. Sou\u010D\u00E1st\u00ED z\u00E1n\u011Btliv\u00E9ho obrazuje granulom s akumulac\u00ED PAS-pozitivn\u00ED amorfn\u00ED hmoty s vysok\u00FDm obsahem fibrinu a bohatou novotvo\u0159enou c\u00E9vn\u00ED s\u00EDt\u00ED. Na z\u00E1klad\u011B postupn\u011B odhalovan\u00FDch poznatk\u016F o mo\u017En\u00E9 etiopatogenezi onemocn\u011Bn\u00ED se odv\u00EDjel i l\u00E9\u010Debn\u00FD postup v dan\u00E9m obdob\u00ED. Celkov\u011B a\u017E dev\u00E1t\u00FD, posledn\u00ED, chirurgick\u00FD v\u00FDkon p\u0159inesl dlouhodobou remisi trvaj\u00EDc\u00ED ji\u017E t\u0159icet m\u011Bs\u00EDc\u016F. Auto\u0159i kombinovali snesen\u00ED granulomu s" . . . "Presentation analyzing etiopathogenesis and management of ligneous conjunctivitis on the basis of clinically difficult particular case"@en . . . "Kr\u00E1sn\u00FD, Jan" . "2"^^ . "RIV/00216208:11120/05:00001453" . "S" . "Dost\u00E1lek, M." . . . "conjunctivitis lignea; plazminogene; heparin; mitomycine C"@en . "4"^^ . . "11120" . "61" . "Conjunctivitis lignea: komplikace vrozen\u00E9ho deficitu plazminogenu (kazuistika)" . "1211-9059" . . "Conjunctivitis lignea: komplikace vrozen\u00E9ho deficitu plazminogenu (kazuistika)" . "Conjunctivitis lignea: komplikace vrozen\u00E9ho deficitu plazminogenu (kazuistika)"@cs . "\u010Cesk\u00E1 a slovensk\u00E1 oftalmologie" . "[C4F9F43025C2]" .