. . . "Systemic sclerosis"@en . "Tom\u010D\u00EDk, Michal" . "V" . . "Systemic sclerosis (SSc) is a rare, chronic connective tissue disease affecting the skin, musculoskeletal system and internal organs. SSc occurs predominantly in women, begins usually in middle age, and the overall survival rate is reduced - 70% of patients survive 10 years. Despite the advances in pharmacotherapy of organ complications and new insights into the pathogenesis of SSc, there is no effective treatment for this serious disorder. The aim of this review article is to introduce this rare disease, its main symptoms, basic principles of diagnosis and current treatment, and contribute to early diagnosis and better prognosis of patients with SSc"@en . "11110" . "[1D7107444FD2]" . "1"^^ . "Syst\u00E9mov\u00E1 sklerodermie" . "RIV/00216208:11110/14:10285275!RIV15-MSM-11110___" . . "16" . "RIV/00216208:11110/14:10285275" . . "autoimmunity; vasculopathy; fibrosis; connective tissue diseases; rheumatic diseases; Systemic sclerosis"@en . "1"^^ . . "Kardiologick\u00E1 revue - Intern\u00ED medic\u00EDna" . "http://www.prolekare.cz/linkout/50157" . "Syst\u00E9mov\u00E1 sklerodermie (SSc) je vz\u00E1cn\u00E9, chronick\u00E9 syst\u00E9mov\u00E9 onemocn\u011Bn\u00ED pojiva postihuj\u00EDc\u00ED k\u016F\u017Ei, pohybov\u00E9 \u00FAstroj\u00ED a vnit\u0159n\u00ED org\u00E1ny. SSc postihuje \u010Dast\u011Bji \u017Eeny, za\u010D\u00EDn\u00E1 obvykle ve st\u0159edn\u00EDm v\u011Bku a celkov\u00E1 doba p\u0159e\u017Eit\u00ED je zkr\u00E1cen\u00E1 - 70 % pacient\u016F p\u0159e\u017E\u00EDv\u00E1 10 let. I p\u0159es pokroky ve farmakoterapii org\u00E1nov\u00FDch komplikac\u00ED a nov\u00E9 poznatky v patogenezi SSc dosud neexistuje \u00FA\u010Dinn\u00E1 l\u00E9\u010Dba tohoto z\u00E1va\u017En\u00E9ho onemocn\u011Bn\u00ED. C\u00EDlem tohoto p\u0159ehledov\u00E9ho \u010Dl\u00E1nku je sezn\u00E1mit \u010Ditatele s touto vz\u00E1cnou nemoc\u00ED, hlavn\u00EDmi p\u0159\u00EDznaky, z\u00E1klady diagnostiky a principy sou\u010Dasn\u00E9 l\u00E9\u010Dby, a p\u0159isp\u011Bt tak ke v\u010Dasn\u00E9 diagn\u00F3ze a k lep\u0161\u00ED progn\u00F3ze pacient\u016F se SSc."@cs . . "2336-288X" . "6"^^ . . . "49225" . "Syst\u00E9mov\u00E1 sklerodermie (SSc) je vz\u00E1cn\u00E9, chronick\u00E9 syst\u00E9mov\u00E9 onemocn\u011Bn\u00ED pojiva postihuj\u00EDc\u00ED k\u016F\u017Ei, pohybov\u00E9 \u00FAstroj\u00ED a vnit\u0159n\u00ED org\u00E1ny. SSc postihuje \u010Dast\u011Bji \u017Eeny, za\u010D\u00EDn\u00E1 obvykle ve st\u0159edn\u00EDm v\u011Bku a celkov\u00E1 doba p\u0159e\u017Eit\u00ED je zkr\u00E1cen\u00E1 - 70 % pacient\u016F p\u0159e\u017E\u00EDv\u00E1 10 let. I p\u0159es pokroky ve farmakoterapii org\u00E1nov\u00FDch komplikac\u00ED a nov\u00E9 poznatky v patogenezi SSc dosud neexistuje \u00FA\u010Dinn\u00E1 l\u00E9\u010Dba tohoto z\u00E1va\u017En\u00E9ho onemocn\u011Bn\u00ED. C\u00EDlem tohoto p\u0159ehledov\u00E9ho \u010Dl\u00E1nku je sezn\u00E1mit \u010Ditatele s touto vz\u00E1cnou nemoc\u00ED, hlavn\u00EDmi p\u0159\u00EDznaky, z\u00E1klady diagnostiky a principy sou\u010Dasn\u00E9 l\u00E9\u010Dby, a p\u0159isp\u011Bt tak ke v\u010Dasn\u00E9 diagn\u00F3ze a k lep\u0161\u00ED progn\u00F3ze pacient\u016F se SSc." . "5" . . "Syst\u00E9mov\u00E1 sklerodermie"@cs . . "Systemic sclerosis"@en . "Syst\u00E9mov\u00E1 sklerodermie"@cs . . . . "Syst\u00E9mov\u00E1 sklerodermie" . . "CZ - \u010Cesk\u00E1 republika" . .