"http://www.prolekare.cz/cesko-slovenska-pediatrie-archiv-cisel?id=3699" . "Wiedermann, J." . "I" . "Zapletalova, J." . "67" . "Turner syndrome (TS) is relatively common disorder with typical features of short stature, gonadal dysgenesis and congenital defects of cardiovascular or uropoetic system. Congenital cardiovascular disease affects approximately 50% of TS individuals and is the major cause of premature mortality due to the aortic dissection. Risk of acute aortic dissection is increased by more than 100- fold in young and middle-aged women with Turner syndrome when compare with the general population. Aortic dissection is usually associated with additional risk factors including bicuspid aortic valve or other abnormalities of the aortic valve, coarctation of aorta or dilatation of the ascending aorta, and systemic arterial hypertension. In recent years, increasing numbers of women with TS have become pregnant via assisted reproduction. The risk for aortic dissection or rupture during pregnancy is 2% or higher. Because of this fact, the Practice Committee of the American Society for Reproductive Medicine recommended in 2005 a careful screening for cardiovascular abnormalities in all TS patients before any planned attempt at pregnancy. Women with any risk factors for aortic dissection should not undertake pregnancy. The review describes the spectrum of cardiovascular defects with particular attention to identifying risk factor for aortic dissection. Authors suggest that all individuals with Turner syndrome require continued cardiovascular monitoring throughout the lifespan including new methods such as magnetic resonance imaging of the heart and great vessels."@en . "Klaskova, E." . . . . . . . . "9"^^ . "Turner\u016Fv syndrom (TS) je relativn\u011B \u010Dast\u00E9 onemocn\u011Bn\u00ED, jeho\u017E hlavn\u00EDmi p\u0159\u00EDznaky jsou mal\u00FD vzr\u016Fst, gonad\u00E1ln\u00ED dysgeneze a vrozen\u00E9 vady kardiovaskul\u00E1rn\u00EDho a uropoetick\u00E9ho syst\u00E9mu. Vrozen\u00E9 srde\u010Dn\u00ED vady postihuj\u00ED p\u0159ibli\u017En\u011B 50 % nositelek TS a jsou hlavn\u00ED p\u0159\u00ED\u010Dinou p\u0159ed\u010Dasn\u00E9 mortality v d\u016Fsledku aort\u00E1ln\u00ED disekce. Mlad\u00E9 \u017Eeny a \u017Eeny ve st\u0159edn\u00EDm v\u011Bku maj\u00ED v\u00EDce ne\u017E 100kr\u00E1t vy\u0161\u0161\u00ED riziko aort\u00E1ln\u00ED disekce ve srovn\u00E1n\u00ED s obecnou populac\u00ED. Aort\u00E1ln\u00ED disekce je obvykle spojena s rizikov\u00FDmi faktory, jako jsou bikuspid\u00E1ln\u00ED aort\u00E1ln\u00ED chlope\u0148 nebo jin\u00E9 abnormality aort\u00E1ln\u00ED chlopn\u011B, koarktace aorty nebo dilatace ascendentn\u00ED aorty a syst\u00E9mov\u00E1 arteri\u00E1ln\u00ED hypertenze. V posledn\u00EDch letech nar\u016Fst\u00E1 po\u010Det \u017Een s TS, kter\u00E9 ot\u011Bhotn\u00ED pomoc\u00ED metod asistovan\u00E9 reprodukce. Riziko disekce nebo ruptury aorty b\u011Bhem gravidity je v\u00EDce ne\u017E 2%. Z tohoto d\u016Fvodu Practice Committee of the American Society for Reproductive Medicine vydal v roce 2005 doporu\u010Den\u00ED prov\u00E9st u v\u0161ech \u017Een s TS, kter\u00E9 pl\u00E1nuj\u00ED t\u011Bhotenstv\u00ED, podrobn\u00E9 screeningov\u00E9 kardiologick\u00E9 vy\u0161et\u0159en\u00ED. \u017Deny s jak\u00FDmkoliv rizikov\u00FDm faktorem pro aort\u00E1ln\u00ED disekci by nem\u011Bly ot\u011Bhotn\u011Bt. P\u0159ehledov\u00FD \u010Dl\u00E1nek popisuje spektrum kardiovaskul\u00E1rn\u00EDch vad se zvl\u00E1\u0161tn\u00EDm d\u016Frazem na zn\u00E1m\u00E9 rizikov\u00E9 faktory pro aort\u00E1ln\u00ED disekci. Auto\u0159i doporu\u010Duj\u00ED u v\u0161ech nositelek Turnerova syndromu celo\u017Eivotn\u00ED kontinu\u00E1ln\u00ED sledov\u00E1n\u00ED kardiologem v\u010Detn\u011B nov\u00FDch metod, jako je magnetick\u00E1 rezonance srdce a velk\u00FDch c\u00E9v."@cs . . "Cardiovascular disease in Turner syndrome"@en . . "RIV/00064203:_____/12:8331" . . . "2" . "Aortic coarctation; Aortic dissection; Aortic size index; Arterial hypertension; Ascending aorta dilatation; Bicuspid aortic valve; Congenital heart defects; Pregnancy; Turner syndrome"@en . . "Tudos, Z." . "\u010Cesko-slovensk\u00E1 pediatrie" . . "CZ - \u010Cesk\u00E1 republika" . "Posti\u017Een\u00ED kardiovaskul\u00E1rn\u00EDho syst\u00E9mu u Turnerova syndromu" . . "Turner\u016Fv syndrom (TS) je relativn\u011B \u010Dast\u00E9 onemocn\u011Bn\u00ED, jeho\u017E hlavn\u00EDmi p\u0159\u00EDznaky jsou mal\u00FD vzr\u016Fst, gonad\u00E1ln\u00ED dysgeneze a vrozen\u00E9 vady kardiovaskul\u00E1rn\u00EDho a uropoetick\u00E9ho syst\u00E9mu. Vrozen\u00E9 srde\u010Dn\u00ED vady postihuj\u00ED p\u0159ibli\u017En\u011B 50 % nositelek TS a jsou hlavn\u00ED p\u0159\u00ED\u010Dinou p\u0159ed\u010Dasn\u00E9 mortality v d\u016Fsledku aort\u00E1ln\u00ED disekce. Mlad\u00E9 \u017Eeny a \u017Eeny ve st\u0159edn\u00EDm v\u011Bku maj\u00ED v\u00EDce ne\u017E 100kr\u00E1t vy\u0161\u0161\u00ED riziko aort\u00E1ln\u00ED disekce ve srovn\u00E1n\u00ED s obecnou populac\u00ED. Aort\u00E1ln\u00ED disekce je obvykle spojena s rizikov\u00FDmi faktory, jako jsou bikuspid\u00E1ln\u00ED aort\u00E1ln\u00ED chlope\u0148 nebo jin\u00E9 abnormality aort\u00E1ln\u00ED chlopn\u011B, koarktace aorty nebo dilatace ascendentn\u00ED aorty a syst\u00E9mov\u00E1 arteri\u00E1ln\u00ED hypertenze. V posledn\u00EDch letech nar\u016Fst\u00E1 po\u010Det \u017Een s TS, kter\u00E9 ot\u011Bhotn\u00ED pomoc\u00ED metod asistovan\u00E9 reprodukce. Riziko disekce nebo ruptury aorty b\u011Bhem gravidity je v\u00EDce ne\u017E 2%. Z tohoto d\u016Fvodu Practice Committee of the American Society for Reproductive Medicine vydal v roce 2005 doporu\u010Den\u00ED prov\u00E9st u v\u0161ech \u017Een s TS, kter\u00E9 pl\u00E1nuj\u00ED t\u011Bhotenstv\u00ED, podrobn\u00E9 screeningov\u00E9 kardiologick\u00E9 vy\u0161et\u0159en\u00ED. \u017Deny s jak\u00FDmkoliv rizikov\u00FDm faktorem pro aort\u00E1ln\u00ED disekci by nem\u011Bly ot\u011Bhotn\u011Bt. P\u0159ehledov\u00FD \u010Dl\u00E1nek popisuje spektrum kardiovaskul\u00E1rn\u00EDch vad se zvl\u00E1\u0161tn\u00EDm d\u016Frazem na zn\u00E1m\u00E9 rizikov\u00E9 faktory pro aort\u00E1ln\u00ED disekci. Auto\u0159i doporu\u010Duj\u00ED u v\u0161ech nositelek Turnerova syndromu celo\u017Eivotn\u00ED kontinu\u00E1ln\u00ED sledov\u00E1n\u00ED kardiologem v\u010Detn\u011B nov\u00FDch metod, jako je magnetick\u00E1 rezonance srdce a velk\u00FDch c\u00E9v." . . "5"^^ . "Cardiovascular disease in Turner syndrome"@en . "Posti\u017Een\u00ED kardiovaskul\u00E1rn\u00EDho syst\u00E9mu u Turnerova syndromu"@cs . "Posti\u017Een\u00ED kardiovaskul\u00E1rn\u00EDho syst\u00E9mu u Turnerova syndromu" . "0069-2328" . "RIV/00064203:_____/12:8331!RIV13-MZ0-00064203" . "\u0160najderov\u00E1, Marta" . "[96E75E4B1376]" . "160194" . . . "Posti\u017Een\u00ED kardiovaskul\u00E1rn\u00EDho syst\u00E9mu u Turnerova syndromu"@cs . . . "1"^^ . . .