"8"^^ . "4" . . "Medicina Sportiva Bohemica et Slovaca" . . "RIV/00064203:_____/11:7344!RIV12-MZ0-00064203" . "Proch\u00E1zka, Michal" . "20" . "[BCEA6C376223]" . "http://www.medvik.cz/link/bmc12001348" . "Case Study of Asymptomatic Long QT Syndrome Detected with Preparticipation Screening"@en . . "Syndrom dlouh\u00E9ho QT intervalu (LQTS) je z\u00E1va\u017En\u00E9 vrozen\u00E9 onemocn\u011Bn\u00ED charakterizovan\u00E9 prodlou\u017Een\u00FDm trv\u00E1n\u00EDm ak\u010Dn\u00EDho potenci\u00E1lu kardiomyocytu na podklad\u011B defektu iontov\u00FDch kan\u00E1l\u016F. V\u00FDsledkem je prodlou\u017Een\u00ED korigovan\u00E9ho intervalu QT na povrchov\u00E9m EKG. Pacienti s LQTS jsou ohro\u017Eeni vznikem polymorfn\u00ED komorov\u00E9 tachykardie torsades de pointes a z toho resultuj\u00EDc\u00ED synkopou nebo n\u00E1hlou arytmickou smrt\u00ED. Zv\u00FD\u0161en\u00E9 riziko je i u asymptomatick\u00FDch p\u0159\u00EDbuzn\u00FDch, kte\u0159\u00ED jsou nosi\u010Di patologick\u00E9 alely. Presentujeme kasuistiku pacienta s klinicky diagnostikovan\u00FDm LQTS, na kter\u00FD bylo vysloveno podez\u0159en\u00ED p\u0159i preventivn\u00ED sportovn\u00ED prohl\u00EDdce na z\u00E1klad\u011B z\u00E1chytu prodlou\u017Een\u00E9ho QT intervalu u jinak asymptomatick\u00E9ho pacienta. Diskutujeme tak\u00E9 \u00FAlohu screeningu v r\u00E1mci sportovn\u00ED populace a jednotliv\u00E1 doporu\u010Den\u00ED pro posuzov\u00E1n\u00ED vhodnosti z\u00E1vodn\u00EDho sportu u pacient\u016F s kardiovaskul\u00E1rn\u00EDm onemocn\u011Bn\u00EDm."@cs . "Janou\u0161ek, Jan" . . "Slab\u00FD, Kry\u0161tof" . "Kasuistika asymptomatick\u00E9ho pacienta se syndromem prodlou\u017Een\u00E9ho QT intervalu zachycen\u00E9ho p\u0159i sportovn\u00ED prohl\u00EDdce"@cs . . "Kubu\u0161, Peter" . . . . "Case Study of Asymptomatic Long QT Syndrome Detected with Preparticipation Screening"@en . "LQTS; long QT syndrome; preparticipation screening"@en . "Kasuistika asymptomatick\u00E9ho pacienta se syndromem prodlou\u017Een\u00E9ho QT intervalu zachycen\u00E9ho p\u0159i sportovn\u00ED prohl\u00EDdce"@cs . . "Kasuistika asymptomatick\u00E9ho pacienta se syndromem prodlou\u017Een\u00E9ho QT intervalu zachycen\u00E9ho p\u0159i sportovn\u00ED prohl\u00EDdce" . . . "5"^^ . "RIV/00064203:_____/11:7344" . "Kasuistika asymptomatick\u00E9ho pacienta se syndromem prodlou\u017Een\u00E9ho QT intervalu zachycen\u00E9ho p\u0159i sportovn\u00ED prohl\u00EDdce" . "CZ - \u010Cesk\u00E1 republika" . "5"^^ . . "1210-5481" . . . . "I" . "207208" . "Syndrom dlouh\u00E9ho QT intervalu (LQTS) je z\u00E1va\u017En\u00E9 vrozen\u00E9 onemocn\u011Bn\u00ED charakterizovan\u00E9 prodlou\u017Een\u00FDm trv\u00E1n\u00EDm ak\u010Dn\u00EDho potenci\u00E1lu kardiomyocytu na podklad\u011B defektu iontov\u00FDch kan\u00E1l\u016F. V\u00FDsledkem je prodlou\u017Een\u00ED korigovan\u00E9ho intervalu QT na povrchov\u00E9m EKG. Pacienti s LQTS jsou ohro\u017Eeni vznikem polymorfn\u00ED komorov\u00E9 tachykardie torsades de pointes a z toho resultuj\u00EDc\u00ED synkopou nebo n\u00E1hlou arytmickou smrt\u00ED. Zv\u00FD\u0161en\u00E9 riziko je i u asymptomatick\u00FDch p\u0159\u00EDbuzn\u00FDch, kte\u0159\u00ED jsou nosi\u010Di patologick\u00E9 alely. Presentujeme kasuistiku pacienta s klinicky diagnostikovan\u00FDm LQTS, na kter\u00FD bylo vysloveno podez\u0159en\u00ED p\u0159i preventivn\u00ED sportovn\u00ED prohl\u00EDdce na z\u00E1klad\u011B z\u00E1chytu prodlou\u017Een\u00E9ho QT intervalu u jinak asymptomatick\u00E9ho pacienta. Diskutujeme tak\u00E9 \u00FAlohu screeningu v r\u00E1mci sportovn\u00ED populace a jednotliv\u00E1 doporu\u010Den\u00ED pro posuzov\u00E1n\u00ED vhodnosti z\u00E1vodn\u00EDho sportu u pacient\u016F s kardiovaskul\u00E1rn\u00EDm onemocn\u011Bn\u00EDm." . . . "Long QT interval syndrome (LQTS) is serious genetic disease characterized by longer action potential duration of cardiomycytes casued by disorder of ion channels function. It is followed by lengthtening of corrected QT interval on resting surface ECG. LQTS patients are at risk of polymorphic ventricular tachycardia \u201Ctorsades de pointes\u201D, syncopy and possibly sudden death. There is also increased risk in asymptomatic carriers. We present a case of patient with clinically diagnosed LQTS suspected in preparticipation with resting ECG."@en . . . "Radvansk\u00FD, Ji\u0159\u00ED" .