. "12" . . "RIV/00064203:_____/10:6615" . "cystick\u00E1 fibr\u00F3za, diagnostika, standardy p\u00E9\u010De, l\u00E9\u010Dba, problematika dosp\u011Bl\u00FDch"@en . . "Cystic fibrosis. Current view on the diagnostics, treatment options and prognosis"@en . "5"^^ . . . "5"^^ . . "CZ - \u010Cesk\u00E1 republika" . "Cystick\u00E1 fibr\u00F3za je nej\u010Dast\u011Bj\u0161\u00EDm autozom\u00E1ln\u011B recesivn\u011B d\u011Bdi\u010Dn\u00FDm onemocn\u011Bn\u00EDm kavkazsk\u00E9 rasy. Onemocn\u011Bn\u00ED m\u00E1 charakter multiorg\u00E1nov\u00E9ho posti\u017Een\u00ED. Je sice nevyl\u00E9\u010Diteln\u00E9, ale st\u00E1le v\u00EDce a l\u00E9pe l\u00E9\u010Diteln\u00E9 s postupn\u00FDm zlep\u0161ov\u00E1n\u00EDm kvality a prodlu\u017Eov\u00E1n\u00EDm d\u00E9lky \u017Eivota nemocn\u00FDch. Progn\u00F3za velmi z\u00E1vis\u00ED na v\u010Dasn\u00E9 diagnostice, multioborov\u00E9m l\u00E9\u010Debn\u00E9m p\u0159\u00EDstupu s vyu\u017Eit\u00EDm nejnov\u011Bj\u0161\u00EDch poznatk\u016F i hlubok\u00FDch zku\u0161enost\u00ED. Komplexn\u00ED l\u00E9\u010Dba je zam\u011B\u0159en\u00E1 na p\u00E9\u010Di o dobrou pr\u016Fchodnost d\u00FDchac\u00EDch cest, p\u00E9\u010Di o dobr\u00FD stav v\u00FD\u017Eivy, boj proti infekci a soustavn\u00E9 vyhled\u00E1v\u00E1n\u00ED a l\u00E9\u010Dbu komplikac\u00ED."@cs . "Postgradu\u00E1ln\u00ED medic\u00EDna" . "252634" . . . "Cystick\u00E1 fibr\u00F3za. Sou\u010Dasn\u00FD pohled na diagnostiku, mo\u017Enosti l\u00E9\u010Dby a progn\u00F3zu" . . "Zemkov\u00E1, Daniela" . . . "Cystick\u00E1 fibr\u00F3za je nej\u010Dast\u011Bj\u0161\u00EDm autozom\u00E1ln\u011B recesivn\u011B d\u011Bdi\u010Dn\u00FDm onemocn\u011Bn\u00EDm kavkazsk\u00E9 rasy. Onemocn\u011Bn\u00ED m\u00E1 charakter multiorg\u00E1nov\u00E9ho posti\u017Een\u00ED. Je sice nevyl\u00E9\u010Diteln\u00E9, ale st\u00E1le v\u00EDce a l\u00E9pe l\u00E9\u010Diteln\u00E9 s postupn\u00FDm zlep\u0161ov\u00E1n\u00EDm kvality a prodlu\u017Eov\u00E1n\u00EDm d\u00E9lky \u017Eivota nemocn\u00FDch. Progn\u00F3za velmi z\u00E1vis\u00ED na v\u010Dasn\u00E9 diagnostice, multioborov\u00E9m l\u00E9\u010Debn\u00E9m p\u0159\u00EDstupu s vyu\u017Eit\u00EDm nejnov\u011Bj\u0161\u00EDch poznatk\u016F i hlubok\u00FDch zku\u0161enost\u00ED. Komplexn\u00ED l\u00E9\u010Dba je zam\u011B\u0159en\u00E1 na p\u00E9\u010Di o dobrou pr\u016Fchodnost d\u00FDchac\u00EDch cest, p\u00E9\u010Di o dobr\u00FD stav v\u00FD\u017Eivy, boj proti infekci a soustavn\u00E9 vyhled\u00E1v\u00E1n\u00ED a l\u00E9\u010Dbu komplikac\u00ED." . "1212-4184" . "7" . "Cystick\u00E1 fibr\u00F3za. Sou\u010Dasn\u00FD pohled na diagnostiku, mo\u017Enosti l\u00E9\u010Dby a progn\u00F3zu" . . "V\u00E1vrov\u00E1, V\u011Bra" . . . "7"^^ . . "Fila, Libor" . . "Cystic fibrosis. Current view on the diagnostics, treatment options and prognosis"@en . "Skalick\u00E1, Veronika" . "[EF561591B43C]" . . . "RIV/00064203:_____/10:6615!RIV11-MZ0-00064203" . "Cystic fibrosis is the most common autosomal recessive disease of the Caucasian population characterised as a chronic multi-systemic affection. Although thus far incurable it has been shown that holistic approach to treatment based on multi-professional centre care provided by trained and experienced health professionals is necessary for optimal management and better outcome leading to life quality and survive improvement. Complex treatment focused on intensive airway clearance, good nutritional status, aggressive anti-infective therapy and continuous searching for complications is essential."@en . . "Cystick\u00E1 fibr\u00F3za. Sou\u010Dasn\u00FD pohled na diagnostiku, mo\u017Enosti l\u00E9\u010Dby a progn\u00F3zu"@cs . "I, Z(MZ0FNM2005)" . . "Cystick\u00E1 fibr\u00F3za. Sou\u010Dasn\u00FD pohled na diagnostiku, mo\u017Enosti l\u00E9\u010Dby a progn\u00F3zu"@cs . "Smol\u00EDkov\u00E1, Libu\u0161e" . . .