"270264" . "Ragheb, J." . . . . "1"^^ . "RIV/00064203:_____/10:6053" . "000274144900010" . . "I, Z(MZ0FNM2005)" . "2" . . "Epilepsia" . . . "Medically intractable epilepsy in Sturge-Weber syndrome is associated with cortical malformation: Implications for surgical therapy" . . "Medically intractable epilepsy in Sturge-Weber syndrome is associated with cortical malformation: Implications for surgical therapy"@en . "Castellano-Sanchez, A." . "US - Spojen\u00E9 st\u00E1ty americk\u00E9" . . "Sturge-Weber syndrome; Epilepsy; Young children; Polymicrogyria; Cortical dysplasia; pediatric epilepsy; fdg-pet; children; disease; abnormalities; dysplasia; migration; perfusion; surgery; mri"@en . . . "[6429042D55E5]" . . . . "0013-9580" . . . "Jayakar, P." . . "RIV/00064203:_____/10:6053!RIV11-MZ0-00064203" . "Purpose: Anecdotal reports have described cortical malformations in epileptic patients with Sturge-Weber syndrome (SWS). No data are available regarding the prevalence and significance of this association. Methods: We reviewed retrospectively the clinical profile, preoperative magnetic resonance imaging (MRI) studies, and pathology reports of all patients with SWS and medically intractable epilepsy evaluated in our epilepsy surgery program between 1979 and 2006. Results: Twelve patients (male/female = 7/5) were identified. Mean age at seizure onset was 11.1 +/- 16.7 months. Seizures occurred daily in seven patients and weekly in five patients. A facial port-wine stain was noted in 10 cases. Eleven patients evidenced developmental delay and eight were hemiparetic. Eight patients underwent excisional surgery for epilepsy (mean age 10.3 +/- 6.5 year), including hemispherectomy (n = 4) and focal cortical resection (n = 4)."@en . "Koehn, M." . "Resnick, T." . . . . "9"^^ . "Morrison, G." . . "Medically intractable epilepsy in Sturge-Weber syndrome is associated with cortical malformation: Implications for surgical therapy"@en . "Duchowny, M." . . . . "Purpose: Anecdotal reports have described cortical malformations in epileptic patients with Sturge-Weber syndrome (SWS). No data are available regarding the prevalence and significance of this association. Methods: We reviewed retrospectively the clinical profile, preoperative magnetic resonance imaging (MRI) studies, and pathology reports of all patients with SWS and medically intractable epilepsy evaluated in our epilepsy surgery program between 1979 and 2006. Results: Twelve patients (male/female = 7/5) were identified. Mean age at seizure onset was 11.1 +/- 16.7 months. Seizures occurred daily in seven patients and weekly in five patients. A facial port-wine stain was noted in 10 cases. Eleven patients evidenced developmental delay and eight were hemiparetic. Eight patients underwent excisional surgery for epilepsy (mean age 10.3 +/- 6.5 year), including hemispherectomy (n = 4) and focal cortical resection (n = 4)." . "11"^^ . "51" . "Kr\u0161ek, Pavel" . . "Medically intractable epilepsy in Sturge-Weber syndrome is associated with cortical malformation: Implications for surgical therapy" . "Maton, B." . . . .