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Statements

Subject Item
n2:RIV%2F00023736%3A_____%2F13%3A00010001%21RIV14-MZ0-00023736
rdf:type
n9:Vysledek skos:Concept
dcterms:description
In 5q- syndrome, high Fli1 mRNA levels in the blood and bone marrow mononuclear cells were found. In DBA, Fli1 expression did not differ from the controls. EKLF mRNA level was significantly decreased in the blood and bone marrow of 5q- syndrome and in all DBA patients. We propose that the elevated Fli1 in 5q- syndrome protects megakaryocytic cells from ribosomal stress contrary to erythroid cells and contributes to effective though dysplastic megakaryopoiesis. In 5q- syndrome, high Fli1 mRNA levels in the blood and bone marrow mononuclear cells were found. In DBA, Fli1 expression did not differ from the controls. EKLF mRNA level was significantly decreased in the blood and bone marrow of 5q- syndrome and in all DBA patients. We propose that the elevated Fli1 in 5q- syndrome protects megakaryocytic cells from ribosomal stress contrary to erythroid cells and contributes to effective though dysplastic megakaryopoiesis.
dcterms:title
Transcription factors Fli1 and EKLF in the differentiation of megakaryocytic and erythroid progenitor in 5q- syndrome and in Diamond-Blackfan anemia Transcription factors Fli1 and EKLF in the differentiation of megakaryocytic and erythroid progenitor in 5q- syndrome and in Diamond-Blackfan anemia
skos:prefLabel
Transcription factors Fli1 and EKLF in the differentiation of megakaryocytic and erythroid progenitor in 5q- syndrome and in Diamond-Blackfan anemia Transcription factors Fli1 and EKLF in the differentiation of megakaryocytic and erythroid progenitor in 5q- syndrome and in Diamond-Blackfan anemia
skos:notation
RIV/00023736:_____/13:00010001!RIV14-MZ0-00023736
n9:predkladatel
n18:ico%3A00023736
n3:aktivita
n17:I n17:P
n3:aktivity
I, P(NT13836)
n3:cisloPeriodika
1
n3:dodaniDat
n14:2014
n3:domaciTvurceVysledku
n5:4787552 n5:6863272 n5:7991401 n5:6881203 n5:3453642 n5:9130969 n5:6961266 n5:6327354 n5:6110886 n5:4073037 n5:4526376
n3:druhVysledku
n16:J
n3:duvernostUdaju
n7:S
n3:entitaPredkladatele
n8:predkladatel
n3:idSjednocenehoVysledku
111542
n3:idVysledku
RIV/00023736:_____/13:00010001
n3:jazykVysledku
n13:eng
n3:klicovaSlova
5q- syndrome; Diamond-Blackfan anemia; EKLF a Fli1; myelodysplastic syndrome; ribosomopathy
n3:klicoveSlovo
n4:EKLF%20a%20Fli1 n4:ribosomopathy n4:myelodysplastic%20syndrome n4:Diamond-Blackfan%20anemia n4:5q-%20syndrome
n3:kodStatuVydavatele
DE - Spolková republika Německo
n3:kontrolniKodProRIV
[B60C74FAAF77]
n3:nazevZdroje
Annals of hematology
n3:obor
n15:FD
n3:pocetDomacichTvurcuVysledku
11
n3:pocetTvurcuVysledku
19
n3:projekt
n11:NT13836
n3:rokUplatneniVysledku
n14:2013
n3:svazekPeriodika
92
n3:tvurceVysledku
Beličková, Monika Čermák, Jaroslav Jonášová, A. Vondráková, J. Fuchs, Ota Neuwirtová, R. Čmejla, Radek Šponerová, Dana Michalová, K. Holická, Monika Vostrý, Martin Hájková, Hana Nováková, Ludmila Pospíšilová, D. Kadlčková, E. Šišková, M. Březinová, Jana Kostečka, Arnošt Hochová, I.
n3:wos
000313068700002
s:issn
0939-5555
s:numberOfPages
8
n19:doi
10.1007/s00277-012-1568-1