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  • Amyloidosis represents a group of diseases with the common feature of extracellular deposition of insoluble patologic proteinaceous substance - amyloid - in tissues. Amyloid deposits can be formed by proteins of different origin and nature, the prerequisite is the ability of these proteins to form cross-beta-pleated sheet conformation. Special staining with Congo red is used to identify amyloid deposits. Progressive extracellular accummulation of amyloid within the tissues produces atrophy of adjacent cells and interference with blood supply play a significant role in organ derangement.
  • Amyloidosis represents a group of diseases with the common feature of extracellular deposition of insoluble patologic proteinaceous substance - amyloid - in tissues. Amyloid deposits can be formed by proteins of different origin and nature, the prerequisite is the ability of these proteins to form cross-beta-pleated sheet conformation. Special staining with Congo red is used to identify amyloid deposits. Progressive extracellular accummulation of amyloid within the tissues produces atrophy of adjacent cells and interference with blood supply play a significant role in organ derangement. (en)
  • Amyloidóza představuje skupinu onemocnění, jejichž společnou vlastností je extracelulární ukládání nerozpustné patologické proteiní substance - amyloidu - ve tkáních. Amyloidní depozita mohou být tvořena proteiny různého původu, jejichž společnou vlastností je schopnost vytvářet beta strukturu. Specielní barvení kongočervení je používáno k identifikaci amyloidních depozit. Progresivní extracelulární akumulace amyloidu ve tkáních vede k jejich atrofii a k cirkulačním poruchám, které mohou vyústit v poškození orgánů. (cs)
Title
  • Amyloidosis from starch to molecular pathology
  • Amyloidosis from starch to molecular pathology (en)
  • Amyloidóza: Od škrobu k molekulární patologii (cs)
skos:prefLabel
  • Amyloidosis from starch to molecular pathology
  • Amyloidosis from starch to molecular pathology (en)
  • Amyloidóza: Od škrobu k molekulární patologii (cs)
skos:notation
  • RIV/00216208:11120/06:00000993!RIV09-MSM-11120___
http://linked.open...avai/riv/aktivita
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  • RIV/00216208:11120/06:00000993
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  • amyloidosis; amyloidogenous proteins; beta structure; organ damage (en)
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  • CZ - Česká republika
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  • [7052CE631FF8]
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  • 4
http://linked.open...iv/tvurceVysledku
  • Mandys, Václav
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  • 1214-4088
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  • 11120
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