About: Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation

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About: Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation Goto Sponge NotDistinct Permalink

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rdf:type	skos:Concept http://linked.opendata.cz/ontology/domain/vavai/Vysledek
Description	Aortic dissection occurs in Turner syndrome with substantially higher frequency in comparison to the general population, and its prevention is one of the main aims of cardiologic follow-up. Findings of cystic medial necrosis in the aortic wall and a high prevalence of aortic dilation suggest that a form of aortopathy exists in Turner syndrome. However, little is known about natural development of aortic dilation prior to dissection. We present a 16-year-old girl with Turner syndrome with a bicuspid aortic valve, aortic stenosis, and dilation of ascending aorta, who underwent annual echocardiographic examinations from early childhood. Significant progressions of proximal aortic dilation occurred twice at the age of 10 and 15 years. Thereafter, another rapid progression was observed during 8 months and within 3 weeks preceding dissection. Acute aortic dissection was diagnosed while the girl was waiting for elective surgery. She was successfully operated. Frequent estimations of aortic diameter in Turner Aortic dissection occurs in Turner syndrome with substantially higher frequency in comparison to the general population, and its prevention is one of the main aims of cardiologic follow-up. Findings of cystic medial necrosis in the aortic wall and a high prevalence of aortic dilation suggest that a form of aortopathy exists in Turner syndrome. However, little is known about natural development of aortic dilation prior to dissection. We present a 16-year-old girl with Turner syndrome with a bicuspid aortic valve, aortic stenosis, and dilation of ascending aorta, who underwent annual echocardiographic examinations from early childhood. Significant progressions of proximal aortic dilation occurred twice at the age of 10 and 15 years. Thereafter, another rapid progression was observed during 8 months and within 3 weeks preceding dissection. Acute aortic dissection was diagnosed while the girl was waiting for elective surgery. She was successfully operated. Frequent estimations of aortic diameter in Turner (en)
Title	Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation (en)
skos:prefLabel	Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation (en)
skos:notation	RIV/00064203:_____/10:6293!RIV11-MZ0-00064203
http://linked.open...avai/riv/aktivita	S Z
http://linked.open...avai/riv/aktivity	S, Z(MZ0FNM2005)
http://linked.open...iv/cisloPeriodika	10
http://linked.open...vai/riv/dodaniDat	2011
http://linked.open...aciTvurceVysledku	Lebl, Jan Šnajderová, Marta Pleskačová, Jana
http://linked.open.../riv/druhVysledku	J - Článek v odborném periodiku
http://linked.open...iv/duvernostUdaju	S - Úplné a pravdivé údaje nepodléhající ochraně podle zvláštních právních předpisů
http://linked.open...titaPredkladatele	Fakultní nemocnice v Motole
http://linked.open...dnocenehoVysledku	247213
http://linked.open...ai/riv/idVysledku	RIV/00064203:_____/10:6293
http://linked.open...riv/jazykVysledku	eng - angličtina
http://linked.open.../riv/klicovaSlova	turner syndrome; aortic dissection; progression of aortic dilation; normal-children; abnormalities; dilatation; dimensions; adults; young (en)
http://linked.open.../riv/klicoveSlovo	dimensions dilatation normal-children progression of aortic dilation abnormalities adults turner syndrome aortic dissection young
http://linked.open...odStatuVydavatele	DE - Spolková republika Německo
http://linked.open...ontrolniKodProRIV	[12B4A442CAEF]
http://linked.open...i/riv/nazevZdroje	European Journal of Pediatrics
http://linked.open...in/vavai/riv/obor	FG
http://linked.open...ichTvurcuVysledku	3 (xsd:int)
http://linked.open...cetTvurcuVysledku	7 (xsd:int)
http://linked.open...UplatneniVysledku	2010
http://linked.open...v/svazekPeriodika	169
http://linked.open...iv/tvurceVysledku	Lebl, Jan Popelová, Jana Šnajderová, Marta Pleskačová, Jana Syrůček, Martin Černý, Štěpán Rücklová, Kristina
http://linked.open...ain/vavai/riv/wos	000281238700019
http://linked.open...n/vavai/riv/zamer	Zdokonalení časné diagnostiky, prevence a léčby těžkých vrozených vývojových vad a chorob geneticky podmíněných či s genetickou dispozicí v prenatální a postnatální fázi vývoje
issn	0340-6199
number of pages	4 (xsd:int)
is http://linked.open...avai/riv/vysledek of	Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation Aortic dissection and rupture in a 16-year-old girl with Turner syndrome following previous progression of aortic dilation

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