About: Translation and proliferation are impaired in Diamond-Blackfan anemia patients     Goto   Sponge   NotDistinct   Permalink

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Description
  • Byla studována rychlost translace a proliferace v bazálním stavu a po aktivaci fytohemaglutininem v mononukleárních buňkách periferní krve u pacientů s DBA. Snížená proliferační i translační rychlost byla zjištěna u všech pacientů s DBA nezávisle na tom, zda mají či nemají mutaci v RPS19. Výsledky naznačují, že terapeutika zvyšující translační účinnost by mohla být použita pro léčbu DBA. (cs)
  • The aims of our work were to study translation and proliferation rates at a basal state and after activation by phytohemaglutinin in peripheral blood mononuclear cells of DBA patients. Impaired proliferation and translation rates were identified in DBA patients independently on RPS19 mutation status. We conclude that therapeutics generally increasing translation might be beneficial for DBA patient treatment.
  • The aims of our work were to study translation and proliferation rates at a basal state and after activation by phytohemaglutinin in peripheral blood mononuclear cells of DBA patients. Impaired proliferation and translation rates were identified in DBA patients independently on RPS19 mutation status. We conclude that therapeutics generally increasing translation might be beneficial for DBA patient treatment. (en)
Title
  • Translation and proliferation are impaired in Diamond-Blackfan anemia patients
  • Translation and proliferation are impaired in Diamond-Blackfan anemia patients (en)
  • Translace a proliferace jsou narušeny u pacientů s Diamondovou-Blackfanovou anémií. (cs)
skos:prefLabel
  • Translation and proliferation are impaired in Diamond-Blackfan anemia patients
  • Translation and proliferation are impaired in Diamond-Blackfan anemia patients (en)
  • Translace a proliferace jsou narušeny u pacientů s Diamondovou-Blackfanovou anémií. (cs)
skos:notation
  • RIV/00023736:_____/04:G0000042!RIV/2005/GA0/L33005/N
http://linked.open.../vavai/riv/strany
  • 20
http://linked.open...avai/riv/aktivita
http://linked.open...avai/riv/aktivity
  • P(GP301/04/P199)
http://linked.open...vai/riv/dodaniDat
http://linked.open...aciTvurceVysledku
http://linked.open.../riv/druhVysledku
http://linked.open...iv/duvernostUdaju
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  • 590658
http://linked.open...ai/riv/idVysledku
  • RIV/00023736:_____/04:G0000042
http://linked.open...riv/jazykVysledku
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  • Diamond-Blackfan anemia;DBA;ribosomal protein S19;RPS19;translation;hypoproliferation (en)
http://linked.open.../riv/klicoveSlovo
http://linked.open...ontrolniKodProRIV
  • [723F99705B54]
http://linked.open...v/mistoKonaniAkce
  • Olomouc
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  • Olomouc
http://linked.open...i/riv/nazevZdroje
  • XVIII. olomoucké hematologické dny s mezinárodní účastí.
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http://linked.open...ichTvurcuVysledku
http://linked.open...cetTvurcuVysledku
http://linked.open...vavai/riv/projekt
http://linked.open...UplatneniVysledku
http://linked.open...iv/tvurceVysledku
  • Pospíšilová, D.
  • Doležalová, Ludmila
  • Lmejlová, Jana
  • Lmejla, Radek
http://linked.open...vavai/riv/typAkce
http://linked.open.../riv/zahajeniAkce
number of pages
http://purl.org/ne...btex#hasPublisher
  • Rubico
https://schema.org/isbn
  • 80-7346-023-8
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