Attributes | Values |
---|
rdf:type
| |
rdfs:seeAlso
| |
Description
| - Diamond-Blackfan anemia (DBA) is a rare congenital red cell aplasia associated with mutations in ribosomal proteins (RP) in 49-71% of cases.1 DBA is a clinically heterogeneous disorder with one-third of patients developing transfusion-acquired iron overload.2 The severity of anemia and transfusion dependency in DBA is comparable to transfusiondependent beta-thalassemia major; however, moderate to severe suppression of erythropoiesis in DBA2 is in contrast to accelerated ineffective erythropoiesis in beta-thalassemia.3,4 The knowledge of systemic iron regulation in DBA is limited.
- Diamond-Blackfan anemia (DBA) is a rare congenital red cell aplasia associated with mutations in ribosomal proteins (RP) in 49-71% of cases.1 DBA is a clinically heterogeneous disorder with one-third of patients developing transfusion-acquired iron overload.2 The severity of anemia and transfusion dependency in DBA is comparable to transfusiondependent beta-thalassemia major; however, moderate to severe suppression of erythropoiesis in DBA2 is in contrast to accelerated ineffective erythropoiesis in beta-thalassemia.3,4 The knowledge of systemic iron regulation in DBA is limited. (en)
|
Title
| - Hepcidin levels in Diamond-Blackfan anemia reflect erythropoietic activity and transfusion dependency
- Hepcidin levels in Diamond-Blackfan anemia reflect erythropoietic activity and transfusion dependency (en)
|
skos:prefLabel
| - Hepcidin levels in Diamond-Blackfan anemia reflect erythropoietic activity and transfusion dependency
- Hepcidin levels in Diamond-Blackfan anemia reflect erythropoietic activity and transfusion dependency (en)
|
skos:notation
| - RIV/00216224:14740/14:00078458!RIV15-MSM-14740___
|
http://linked.open...avai/riv/aktivita
| |
http://linked.open...avai/riv/aktivity
| - I, P(ED0030/01/01), P(GAP305/11/1745), R, S
|
http://linked.open...iv/cisloPeriodika
| |
http://linked.open...vai/riv/dodaniDat
| |
http://linked.open...aciTvurceVysledku
| |
http://linked.open.../riv/druhVysledku
| |
http://linked.open...iv/duvernostUdaju
| |
http://linked.open...titaPredkladatele
| |
http://linked.open...dnocenehoVysledku
| |
http://linked.open...ai/riv/idVysledku
| - RIV/00216224:14740/14:00078458
|
http://linked.open...riv/jazykVysledku
| |
http://linked.open.../riv/klicovaSlova
| - Diamond Blackfan anemia; hepcidin levels; erythropoietic activity; transfusion dependency (en)
|
http://linked.open.../riv/klicoveSlovo
| |
http://linked.open...odStatuVydavatele
| |
http://linked.open...ontrolniKodProRIV
| |
http://linked.open...i/riv/nazevZdroje
| |
http://linked.open...in/vavai/riv/obor
| |
http://linked.open...ichTvurcuVysledku
| |
http://linked.open...cetTvurcuVysledku
| |
http://linked.open...vavai/riv/projekt
| |
http://linked.open...UplatneniVysledku
| |
http://linked.open...v/svazekPeriodika
| |
http://linked.open...iv/tvurceVysledku
| - Pospíšilová, Dagmar
- Radová, Lenka
- Hajdúch, Marian
- Dzubak, P.
- Divoký, Vladimír
- Mihal, V.
- Holub, D.
- Hadacova, I.
- Horvathova, M.
- Houda, J.
- Sulovska, L.
- Zidova, Z.
|
http://linked.open...ain/vavai/riv/wos
| |
issn
| |
number of pages
| |
http://bibframe.org/vocab/doi
| - 10.3324/haematol.2014.104034
|
http://localhost/t...ganizacniJednotka
| |