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  • Fahr's disease is characterized by idiopathic calcification of the basal ganglia and other brain regions. Clinically it may be accompanied by extrapyramidal and behavioural disorders. In Fahr's syndrome, the same pathology si due to another well-defined disease. Calcium/phosphate metabolic disorders, e.g. hypoparathyroidism or pseudohyperparathyroidism, may be involved. Here, we report a case of 62-years-old man presenting with severe dementia but only mild movement disorders and mild calcium metabolism abnormalities.
  • Fahr's disease is characterized by idiopathic calcification of the basal ganglia and other brain regions. Clinically it may be accompanied by extrapyramidal and behavioural disorders. In Fahr's syndrome, the same pathology si due to another well-defined disease. Calcium/phosphate metabolic disorders, e.g. hypoparathyroidism or pseudohyperparathyroidism, may be involved. Here, we report a case of 62-years-old man presenting with severe dementia but only mild movement disorders and mild calcium metabolism abnormalities. (en)
  • Fahrova nemoc je charakterizovaná idiopatickou kalcifikací v basálních gangliích, ale i v jiných oblastech mozku. Klinicky se onemocnění projevuje extrapyramidovými a neuropsychiatrickými příznaky. Fahrův syndrom je charakterizován taktéž kalcifikací v bazálních ganglií, ale v důsledku jiného onemocnění. Především může být spojen s poruchou metabolismu kalcia a fosforu, např.: při parathyroidismu nebo pseudohyperparathyroidismu. V naší kazuistice prezentujeme 62- letého muže s výrazným narušením kognitivních funkcí s mírnou extrapyramidovou symptomatologií a s lehkým narušením metabolismu kalcia. (cs)
Title
  • Dementia in a patient with Fahr's syndrome
  • Demence u pacienta s Fahrovým syndromem (cs)
  • Dementia in a patient with Fahr's syndrome (en)
skos:prefLabel
  • Dementia in a patient with Fahr's syndrome
  • Demence u pacienta s Fahrovým syndromem (cs)
  • Dementia in a patient with Fahr's syndrome (en)
skos:notation
  • RIV/00216208:11150/08:00106972!RIV09-MSM-11150___
http://linked.open...avai/riv/aktivita
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  • S
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  • 4
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  • 362456
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  • RIV/00216208:11150/08:00106972
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  • Fahr's syndrome; basal ganglia calcification; executive functions; dementia; hypoparathyroidism (en)
http://linked.open.../riv/klicoveSlovo
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  • SE - Švédské království
http://linked.open...ontrolniKodProRIV
  • [C5B75A18D1C7]
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  • Neuroendocrinology Letters
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  • 29
http://linked.open...iv/tvurceVysledku
  • Horáček, Jiří
  • Masopust, Jiří
  • Vališ, Martin
  • Konupčíková, Kateřina
http://linked.open...ain/vavai/riv/wos
  • 000259774200007
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  • 0172-780X
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  • 11150
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