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Description
  • We present the case of a 75-year-old woman who was operated because of significant aortic stenosis. Microscopic examination of the valve showed not only degenerative changes but, in addition, extensive deposition of dark brown pigment. The suspicion of alcaptonuria (ochronosis) was subsequently confirmed by detection of high levels of homogentisic acid in urine.
  • We present the case of a 75-year-old woman who was operated because of significant aortic stenosis. Microscopic examination of the valve showed not only degenerative changes but, in addition, extensive deposition of dark brown pigment. The suspicion of alcaptonuria (ochronosis) was subsequently confirmed by detection of high levels of homogentisic acid in urine. (en)
  • Prezentujeme případ 75leté ženy, která byla operována pro významnou aortální stenózu. Mikroskopické vyšetření chlopně prokázalo kromě degenerativních změn také ložiska tmavě hnědého pigmentu. Bylo vysloveno podezření na alkaptonurii (ochronózu), která byla následně potvrzena nálezem výrazně zvýšené koncentrace kyseliny homogentisové v moči. (cs)
Title
  • Black aortic valve - ochronosis
  • Black aortic valve - ochronosis (en)
  • Černá aortální chlopeň - ochronóza (cs)
skos:prefLabel
  • Black aortic valve - ochronosis
  • Black aortic valve - ochronosis (en)
  • Černá aortální chlopeň - ochronóza (cs)
skos:notation
  • RIV/00216208:11150/08:00106857!RIV09-MSM-11150___
http://linked.open...avai/riv/aktivita
http://linked.open...avai/riv/aktivity
  • S
http://linked.open...iv/cisloPeriodika
  • 3
http://linked.open...vai/riv/dodaniDat
http://linked.open...aciTvurceVysledku
http://linked.open.../riv/druhVysledku
http://linked.open...iv/duvernostUdaju
http://linked.open...titaPredkladatele
http://linked.open...dnocenehoVysledku
  • 358253
http://linked.open...ai/riv/idVysledku
  • RIV/00216208:11150/08:00106857
http://linked.open...riv/jazykVysledku
http://linked.open.../riv/klicovaSlova
  • alkaptonuria; ochronosis; heart; aortic stenosis (en)
http://linked.open.../riv/klicoveSlovo
http://linked.open...odStatuVydavatele
  • DK - Dánské království
http://linked.open...ontrolniKodProRIV
  • [D593B2021FF9]
http://linked.open...i/riv/nazevZdroje
  • Acta Pathologica, Microbiologica et Immunologica Scandinavica
http://linked.open...in/vavai/riv/obor
http://linked.open...ichTvurcuVysledku
http://linked.open...cetTvurcuVysledku
http://linked.open...UplatneniVysledku
http://linked.open...v/svazekPeriodika
  • 116
http://linked.open...iv/tvurceVysledku
  • Laco, Jan
  • Šteiner, Ivo
  • Špaček, Josef
  • Kubíček, Vlastimil
http://linked.open...ain/vavai/riv/wos
  • 000261975000010
issn
  • 0903-4641
number of pages
http://localhost/t...ganizacniJednotka
  • 11150
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