About: Ostraya zadnyaya mul'tifokal'naya plakoidnyye pigment epiteliopatii u rebenka. Klinicheskij sluchaj     Goto   Sponge   NotDistinct   Permalink

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  • Avtory predstavlyayut redkiy sluchay doklad APMPPE v 12- letney devochki s podrobnym dokumental'no nakhozhdeniya vospalitel'nykh izmeneniy v makuly , chto privodit k umen'sheniyu BCVA . Posle sistemnogo i mestnogo steroidovBCVA uluchshilos' bystro , khotya izmeneniya v IS / OS styke i narusheniya v NPP sloya ostalis'. V oftal'mologicheskiye nakhodki ne soprovozhdalis' ni sistemnykh priznakov ili diseases.Introduction APMPPE yavlyayetsya ochen' redkim dvustoronneye zabolevaniye, kotoroye bylo vpervyye opisano Gass JDM v 1968 godu. Okolo 30 % patsiyentov imeyut vvodnaya pokhozhiy na simptomy grippa . Redko , APMPPE mozhet byt' svyazano s tserebral'nyy vaskulit , vospaleniye shchitovidnoy zhelezy, granulematoz Vegenera ili mikrososudov nefropatii. Bol'shinstvo patsiyentov (80%) ne trebuyut lecheniya , i sistemnyye steroidy zarezervirovany dlya patsiyentov s porazhennoy pyaten . Prognoz na APMPPE khorosho , yesli makulyarnoy oblasti ne vliyayet.
  • The authors present a rare case report of APMPPE in a 12-year- old girl with a detailed documented finding of inflammatory changes in the macula, leading to a decrease in BCVA. After systemic and local steroids the BCVA improved promptly, although changes in the IS/OS junction and irregularities in the RPE layer remained. The ophthalmological findings were not accompanied by any systemic signs or diseases.Introduction APMPPE is a very rare bilateral disease which was first described by Gass JDM in 1968 . Around 30% of the patients have a prodrome similar to flu symptoms. Rarely, APMPPE can be associated with cerebral vasculitis, inflammation of the thyroid gland, Wegener's granulomatosis or microvascular nephropathy. The majority of patients (80%) do not require treatment, and systemic steroids are reserved for patients with affected maculae . The prognosis of the APMPPE is good unless the macular region is affected. (en)
Title
  • Ostraya zadnyaya mul'tifokal'naya plakoidnyye pigment epiteliopatii u rebenka. Klinicheskij sluchaj
  • Acute Posterior Multifocal Placoid Pigment Epitheliopathy in a Child (en)
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  • Ostraya zadnyaya mul'tifokal'naya plakoidnyye pigment epiteliopatii u rebenka. Klinicheskij sluchaj
  • Acute Posterior Multifocal Placoid Pigment Epitheliopathy in a Child (en)
skos:notation
  • RIV/00179906:_____/13:10193003!RIV14-MZ0-00179906
http://linked.open...avai/riv/aktivita
http://linked.open...avai/riv/aktivity
  • I
http://linked.open...iv/cisloPeriodika
  • 2
http://linked.open...vai/riv/dodaniDat
http://linked.open...aciTvurceVysledku
http://linked.open.../riv/druhVysledku
http://linked.open...iv/duvernostUdaju
http://linked.open...titaPredkladatele
http://linked.open...dnocenehoVysledku
  • 94785
http://linked.open...ai/riv/idVysledku
  • RIV/00179906:_____/13:10193003
http://linked.open...riv/jazykVysledku
http://linked.open.../riv/klicovaSlova
  • macular edema; SD-OCT; Acute Posterior Multifocal Placoid Pigment Epitheliopathy (en)
http://linked.open.../riv/klicoveSlovo
http://linked.open...odStatuVydavatele
  • RU - Ruská federace
http://linked.open...ontrolniKodProRIV
  • [1B300069B471]
http://linked.open...i/riv/nazevZdroje
  • Ophthalmologija
http://linked.open...in/vavai/riv/obor
http://linked.open...ichTvurcuVysledku
http://linked.open...cetTvurcuVysledku
http://linked.open...UplatneniVysledku
http://linked.open...v/svazekPeriodika
  • 10
http://linked.open...iv/tvurceVysledku
  • Burova, Mariya
  • Rozsíval, Pavel
  • Langrová, Hana
  • Rencová, Eva
  • Studnička, Jan
  • Stepanov, Alexandr
  • Breznayová, Jana
issn
  • 1816-5095
number of pages
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