About: Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature

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About: Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature Goto Sponge NotDistinct Permalink

An Entity of Type : http://linked.opendata.cz/ontology/domain/vavai/Vysledek, within Data Space : linked.opendata.cz associated with source document(s)

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rdf:type	skos:Concept http://linked.opendata.cz/ontology/domain/vavai/Vysledek
Description	Mycosis fungoides (MF) displays a broad spectrum of clinical, histological, and phenotypic variants with different prognostic impact. CD8(+)CD56(+) MF is very rare. So far, only 5 patients with CD8(+)CD56(+) MF were reported to date. All of the previously described patients with this phenotypic variant were adults at the time of diagnosis and often manifested with widespread poikilodermatous skin lesions. Here we describe the clinicopathological features of a juvenile form of CD8(+)CD56(+) non-poikilodermatous MF in a 10-year-old girl. In our patient, the disease displayed an indolent course and excellent prognosis with complete remission after treatment with UV light, topical steroids, and methotrexate. The differential diagnosis of CD8(+) epidermotropic lymphocytic infiltrates in children is discussed, and the cases of CD8(+)CD56(+) MF reported in the literature are reviewed. Mycosis fungoides (MF) displays a broad spectrum of clinical, histological, and phenotypic variants with different prognostic impact. CD8(+)CD56(+) MF is very rare. So far, only 5 patients with CD8(+)CD56(+) MF were reported to date. All of the previously described patients with this phenotypic variant were adults at the time of diagnosis and often manifested with widespread poikilodermatous skin lesions. Here we describe the clinicopathological features of a juvenile form of CD8(+)CD56(+) non-poikilodermatous MF in a 10-year-old girl. In our patient, the disease displayed an indolent course and excellent prognosis with complete remission after treatment with UV light, topical steroids, and methotrexate. The differential diagnosis of CD8(+) epidermotropic lymphocytic infiltrates in children is discussed, and the cases of CD8(+)CD56(+) MF reported in the literature are reviewed. (en)
Title	Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature (en)
skos:prefLabel	Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature Pediatric CD8(+)CD56(+) Non-poikilodermatous Mycosis Fungoides: Case Report and Review of the Literature (en)
skos:notation	RIV/00216208:11140/14:10271585!RIV15-MSM-11140___
http://linked.open...avai/riv/aktivita	I
http://linked.open...avai/riv/aktivity	I
http://linked.open...iv/cisloPeriodika	7
http://linked.open...vai/riv/dodaniDat	2015
http://linked.open...aciTvurceVysledku	Kazakov, Dmitry
http://linked.open.../riv/druhVysledku	J - Článek v odborném periodiku
http://linked.open...iv/duvernostUdaju	S - Úplné a pravdivé údaje nepodléhající ochraně podle zvláštních právních předpisů
http://linked.open...titaPredkladatele	Univerzita Karlova v Praze / Lékařská fakulta v Plzni
http://linked.open...dnocenehoVysledku	36040
http://linked.open...ai/riv/idVysledku	RIV/00216208:11140/14:10271585
http://linked.open...riv/jazykVysledku	eng - angličtina
http://linked.open.../riv/klicovaSlova	child; pediatric; juvenile; natural killer; CD56; cytotoxic lymphoma; mycosis fungoides; cutaneous lymphoma (en)
http://linked.open.../riv/klicoveSlovo	CD56 natural killer mycosis fungoides cytotoxic lymphoma pediatric cutaneous lymphoma child - threat - divorce - domestic violence - abandonment - adoption juvenile
http://linked.open...odStatuVydavatele	US - Spojené státy americké
http://linked.open...ontrolniKodProRIV	[AA181AA24EB4]
http://linked.open...i/riv/nazevZdroje	American Journal of Dermatopathology
http://linked.open...in/vavai/riv/obor	FP
http://linked.open...ichTvurcuVysledku	1 (xsd:int)
http://linked.open...cetTvurcuVysledku	4 (xsd:int)
http://linked.open...UplatneniVysledku	2014
http://linked.open...v/svazekPeriodika	36
http://linked.open...iv/tvurceVysledku	Kazakov, Dmitry Kempf, Werner Metze, Dieter Broekaert, Sigrid M. C.
http://linked.open...ain/vavai/riv/wos	000338531700014
issn	0193-1091
number of pages	5 (xsd:int)
http://localhost/t...ganizacniJednotka	11140

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