About: Thrombocytopenic microangiopatic disorders - etiology, pathofysiology and diagnostic     Goto   Sponge   NotDistinct   Permalink

An Entity of Type : http://linked.opendata.cz/ontology/domain/vavai/Projekt, within Data Space : linked.opendata.cz associated with source document(s)

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Description
  • We will study molecular-genetic of atypical HUS: establish an assay for measurement of factor H, screen mutations in gene for factor H and look for other possible causes of disease. We will study relationship of ADAMTS13 and BMT-associated TMA, its treatment and other causes of microangiopatic syndromes. (en)
  • V rámci molekulárně-genetické diagnostiky atypického HUS budeme zavádět metodiky na stanovení hladiny H-faktoru, metodiky na DNA analýzu genu pro H-faktor a další ukazatele průběhu remise i onemocnění. V rámci mikroangiopatických syndromů v souvislosti s TKD budeme sledovat hladinu ADAMTS13 a jeho funkci, aktivaci endotelu a jejich vztah k léčbě.
Title
  • Thrombocytopenic microangiopatic disorders - etiology, pathofysiology and diagnostic (en)
  • Konsumpční trombotické mikroangiopatie - etiologie, patofyziologie a diagnostika
skos:notation
  • NR9258
http://linked.open...avai/cep/aktivita
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  • TMA; hemolytic uremic syndrome; factor H; TTP; bone marrow transplant; micro-vascular thrombi; complement activation; metalloproteases (en)
http://linked.open...ep/partnetrHlavni
http://linked.open...inujicichPrijemcu
http://linked.open...cep/pocetPrijemcu
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  • The results of this project are very poor. (en)
  • Výstupy projektu jsou velmi chabé. (cs)
http://linked.open...tniCyklusProjektu
http://linked.open.../cep/klicoveSlovo
  • TMA
  • TTP
  • bone marrow transplant
  • complement activation
  • factor H
  • hemolytic uremic syndrome
  • micro-vascular thrombi
is http://linked.open...vavai/cep/projekt of
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